{"id":16536,"date":"2020-04-28T17:02:22","date_gmt":"2020-04-28T20:02:22","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/wiki\/patologia-del-xantogranuloma-juvenil\/"},"modified":"2020-04-30T21:34:04","modified_gmt":"2020-05-01T00:34:04","slug":"patologia-del-xantogranuloma-juvenil","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-xantogranuloma-juvenil\/","title":{"rendered":"Pathology of juvenile xanthogranuloma"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_87_1 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contents<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-xantogranuloma-juvenil\/#Introduccion\" >Introduction<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-xantogranuloma-juvenil\/#Histologia-de-xantogranuloma-juvenil\" >Histolog\u00eda de xantogranuloma juvenil<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-xantogranuloma-juvenil\/#Patologia-del-xantogranuloma-juvenil\" >Pathology of juvenile xanthogranuloma<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-xantogranuloma-juvenil\/#Estudios-especiales-para-xantogranuloma-juvenil\" >Estudios especiales para xantogranuloma juvenil<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-xantogranuloma-juvenil\/#Diagnostico-diferencial-para-xantogranuloma-juvenil\" >Diagn\u00f3stico diferencial para xantogranuloma juvenil<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Introduccion\"><\/span>Introduction<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span class=\"term\" data-term-id=\"1610\">Youth<\/span> El xantogranuloma generalmente se presenta en individuos m\u00e1s j\u00f3venes como rosa suave o amarillo <span class=\"term\" data-term-id=\"367\">nodules<\/span>.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Histologia-de-xantogranuloma-juvenil\"><\/span>\n<span class=\"term\" data-term-id=\"128\">Histology<\/span> juvenile xanthogranuloma<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>En el xantogranuloma juvenil, el <span class=\"term\" data-term-id=\"164\">injury<\/span> comienza como un denso <span class=\"term\" data-term-id=\"1480\">lymphohistiocytic<\/span> <span class=\"term\" data-term-id=\"893\">proliferation<\/span> of <span class=\"term\" data-term-id=\"61\">dermis<\/span> con raro <span class=\"term\" data-term-id=\"739\">giant cells<\/span>. A medida que evoluciona, el <span class=\"term\" data-term-id=\"52\">dermal<\/span> <span class=\"term\" data-term-id=\"289\">tumor<\/span> contiene una poblaci\u00f3n de espumosos <span class=\"term\" data-term-id=\"858\">histiocytes<\/span> y c\u00e9lulas gigantes (figuras 1\u20133). Las c\u00e9lulas gigantes de Touton son bastante caracter\u00edsticas del xantogranuloma juvenil (mejor visto en la figura 3). Estas c\u00e9lulas contienen un anillo de <span class=\"term\" data-term-id=\"729\">nuclei<\/span> rodeando una central <span class=\"term\" data-term-id=\"1607\">homogeneous<\/span> <span class=\"term\" data-term-id=\"838\">cytoplasm<\/span>, mientras que el citoplasma espumoso rodea los n\u00facleos. M\u00e1s tarde, las c\u00e9lulas se vuelven m\u00e1s espinosas y fibrohistioc\u00edticas.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Patologia-del-xantogranuloma-juvenil\"><\/span>Pathology of juvenile xanthogranuloma<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='juvenile-xanthogranuloma-figure-1-3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-1496843-7219322' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/juvenile-xanthogranuloma-figure-1-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-1496843.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='juvenile-xanthogranuloma-figure-2-3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-1438830-6061708' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/juvenile-xanthogranuloma-figure-2-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-1438830.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='juvenile-xanthogranuloma-figure-3-3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-5221339-6866764' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/juvenile-xanthogranuloma-figure-3-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-5221339.jpg'>\n<\/div>\n<p class=\"p-small\">figure 3<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Estudios-especiales-para-xantogranuloma-juvenil\"><\/span>Estudios especiales para xantogranuloma juvenil<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span class=\"term\" data-term-id=\"1421\">Immunohistochemistry<\/span> puede ser usado. T\u00edpicamente, el tumor es positivo con CD68, alfa-1-anticimotripsina, lisozima, vimentina y factor XIIIa. Las manchas negativas \u00fatiles incluyen S100 y CD1a.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Diagnostico-diferencial-para-xantogranuloma-juvenil\"><\/span>\n<span class=\"term\" data-term-id=\"813\">Differential diagnosis<\/span> para xantogranuloma juvenil<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<ul>\n<li>\n<p>El dermatofibroma generalmente carece de c\u00e9lulas gigantes de Touton y tiene una densidad densa <span class=\"term\" data-term-id=\"1185\">collagen<\/span> <span class=\"term\" data-term-id=\"1655\">stroma<\/span>, patr\u00f3n de crecimiento tormentoso y, a menudo, una capa suprayacente <span class=\"term\" data-term-id=\"247\">pseudoepitheliomatous<\/span> <span class=\"term\" data-term-id=\"136\">hyperplasia<\/span>.<\/li>\n<li>Los xantomas muestran histiocitos espumosos m\u00e1s uniformes y se presentan con mayor frecuencia en multiplicidad. la <span class=\"term\" data-term-id=\"1064\">polymorphous<\/span> <span class=\"term\" data-term-id=\"541\">infiltrate<\/span> t\u00edpicamente visto en xantogranuloma juvenil generalmente est\u00e1 ausente.<\/li>\n<li>Langerhans cell <span class=\"term\" data-term-id=\"1346\">histiocytosis<\/span> t\u00edpicamente muestra tinci\u00f3n con S100 + y CD1a +.<\/li>\n<li>\n<p>El reticulohistiocitoma est\u00e1 compuesto de histiocitos con <span class=\"term\" data-term-id=\"449\">eosinophilic<\/span> o citoplasma de vidrio esmerilado.<\/li>\n<\/ul>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Introducci\u00f3n Juvenil El xantogranuloma generalmente se presenta en individuos m\u00e1s j\u00f3venes como rosa suave o amarillo n\u00f3dulos. Histolog\u00eda de xantogranuloma juvenil En el xantogranuloma juvenil, el lesi\u00f3n comienza como un&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[205],"class_list":["post-16536","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones","tag-patologia"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/16536","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=16536"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/16536\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=16536"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=16536"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=16536"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}