{"id":6667,"date":"2020-04-22T16:11:50","date_gmt":"2020-04-22T19:11:50","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/paniculitis-histiocitica-citofagica\/"},"modified":"2020-04-27T17:10:03","modified_gmt":"2020-04-27T20:10:03","slug":"paniculitis-histiocitica-citofagica","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/","title":{"rendered":"Cytophageal histiocytic panniculitis"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_87_1 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contents<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/#Que-es-paniculitis\" >What is panniculitis?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFQue-es-citofagico-histiocitico-paniculitis\" >\u00bfQu\u00e9 es citof\u00e1gico? histioc\u00edtico paniculitis?<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/#Paniculitis-histiocitica-citofagica\" >Cytophageal histiocytic panniculitis<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-paniculitis-histiocitica-citofagica\" >\u00bfCu\u00e1les son las caracter\u00edsticas cl\u00ednicas de la paniculitis histioc\u00edtica citof\u00e1gica?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFCual-es-la-causa-de-la-paniculitis-histiocitica-citofagica\" >\u00bfCu\u00e1l es la causa de la paniculitis histioc\u00edtica citof\u00e1gica?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFComo-se-diagnostica-la-paniculitis-histiocitica-citofagica\" >\u00bfC\u00f3mo se diagnostica la paniculitis histioc\u00edtica citof\u00e1gica?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFCual-es-el-tratamiento-de-la-paniculitis-histiocitica-citofagica\" >\u00bfCu\u00e1l es el tratamiento de la paniculitis histioc\u00edtica citof\u00e1gica?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Que-es-paniculitis\"><\/span>What is it <span class=\"term\" data-term-id=\"213\">panniculitis<\/span>?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Panniculitis<span> es un t\u00e9rmino que generalmente se refiere a un trastorno de la <span class=\"term\" data-term-id=\"900\">subcutaneous<\/span> grease.<\/span><\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-es-citofagico-histiocitico-paniculitis\"><\/span>\u00bfQu\u00e9 es citof\u00e1gico? <span class=\"term\" data-term-id=\"859\">histiocytic<\/span> paniculitis?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La paniculitis histioc\u00edtica citof\u00e1gica es un <span class=\"term\" data-term-id=\"490\">inflammatory<\/span> condici\u00f3n de la grasa subcut\u00e1nea. Se diagnostica despu\u00e9s de un <span class=\"term\" data-term-id=\"24\">biopsy<\/span> ha detectado anormal <span class=\"term\" data-term-id=\"858\">histiocytes<\/span> que envuelven otras c\u00e9lulas (como los gl\u00f3bulos rojos y blancos).<\/p>\n<p>La paniculitis histioc\u00edtica citof\u00e1gica tambi\u00e9n afecta a otros \u00f3rganos y es una afecci\u00f3n potencialmente mortal.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Paniculitis-histiocitica-citofagica\"><\/span>Cytophageal histiocytic panniculitis<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='cytophagic-panniculitis1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisinkildg1xq-3541678-6390383' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/cytophagic-panniculitis1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDg1XQ-3541678.jpg'>\n<\/div>\n<p class=\"p-small\">Cytophageal histiocytic panniculitis<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='cytophagic-panniculitis2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-5382260-4292604' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/cytophagic-panniculitis2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-5382260.jpg'>\n<\/div>\n<p class=\"p-small\">Cytophageal histiocytic panniculitis<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='cytophagic-panniculitis3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-6540464-5242445' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/cytophagic-panniculitis3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-6540464.jpg'>\n<\/div>\n<p class=\"p-small\">Cytophageal histiocytic panniculitis<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-paniculitis-histiocitica-citofagica\"><\/span>\u00bfCu\u00e1les son las caracter\u00edsticas cl\u00ednicas de la paniculitis histioc\u00edtica citof\u00e1gica?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La paniculitis histioc\u00edtica citof\u00e1gica se presenta con dolor subcut\u00e1neo <span class=\"term\" data-term-id=\"367\">nodules<\/span> en m\u00faltiples sitios y <span class=\"term\" data-term-id=\"380\">systemic<\/span> symptoms<\/p>\n<ul>\n<li>El paciente se siente mal y tiene un <span class=\"term\" data-term-id=\"1176\">fever<\/span>.<\/li>\n<li>Hay una disminuci\u00f3n en las c\u00e9lulas y <span class=\"term\" data-term-id=\"616\">platelets<\/span> en la sangre.<\/li>\n<li>El h\u00edgado y el bazo est\u00e1n agrandados.<\/li>\n<li>\n<span class=\"term\" data-term-id=\"1759\">Progressive<\/span> Se desarrolla insuficiencia hep\u00e1tica.<\/li>\n<\/ul>\n<p>La muerte, cuando ocurre, se asocia con sangrado de los tractos gastrointestinal, urinario y respiratorio y hacia la piel.  <\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-la-causa-de-la-paniculitis-histiocitica-citofagica\"><\/span>\u00bfCu\u00e1l es la causa de la paniculitis histioc\u00edtica citof\u00e1gica?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La paniculitis histioc\u00edtica citof\u00e1gica se desencadena por un <span class=\"term\" data-term-id=\"145\">infection<\/span> en aproximadamente el 50% de los casos<span style=\"font-size: 1rem;\">. Este suele ser uno de los virus del herpes. La enfermedad ocurre en pacientes con funci\u00f3n inmune alterada debido a <\/span>immunodeficiency<span style=\"font-size: 1rem;\">, a <span class=\"term\" data-term-id=\"691\">autoimmune<\/span> illness or <span class=\"term\" data-term-id=\"1522\">hematological<\/span> disease.<\/span><\/p>\n<p>Subcutaneous <span class=\"term\" data-term-id=\"631\">T cell<\/span> <span class=\"term\" data-term-id=\"976\">lymphoma<\/span> Tambi\u00e9n puede presentarse con paniculitis histioc\u00edtica citof\u00e1gica.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-diagnostica-la-paniculitis-histiocitica-citofagica\"><\/span>\u00bfC\u00f3mo se diagnostica la paniculitis histioc\u00edtica citof\u00e1gica?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Biopsia de una subcut\u00e1nea. <span class=\"term\" data-term-id=\"198\">nodule<\/span> muestra histiocitos citof\u00e1gicos y c\u00e9lulas inflamatorias asociadas con la descomposici\u00f3n y <span class=\"term\" data-term-id=\"120\">hemorrhage<\/span> en grasa subcut\u00e1nea Anormal <span class=\"term\" data-term-id=\"421\">lymphocytes<\/span> puede conducir a un diagn\u00f3stico de linfoma de c\u00e9lulas T. <\/p>\n<p>Investigaciones adicionales pueden mostrar da\u00f1o a otros \u00f3rganos y una tendencia a sangrar. Puede haber evidencia de una infecci\u00f3n previa, como un virus del herpes, y de una funci\u00f3n inmune alterada. Si se diagnostica linfoma de c\u00e9lulas T, la estadificaci\u00f3n puede encontrar evidencia de linfoma en el <span class=\"term\" data-term-id=\"1775\">lymph nodes<\/span> y en otra parte<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-el-tratamiento-de-la-paniculitis-histiocitica-citofagica\"><\/span>\u00bfCu\u00e1l es el tratamiento de la paniculitis histioc\u00edtica citof\u00e1gica?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La paniculitis histioc\u00edtica citof\u00e1gica suele ser letal si no se trata.  <\/p>\n<p>El tratamiento sintom\u00e1tico consiste en transfusi\u00f3n y terapia con corticosteroides. Se ha informado que el etop\u00f3sido y la ciclosporina son \u00fatiles en algunos casos. Algunos autores recomiendan que la paniculitis histioc\u00edtica citof\u00e1gica se trate con poliquimioterapia tipo CHOP. Se han obtenido buenos resultados con dosis intravenosas altas. <span class=\"term\" data-term-id=\"427\">immunoglobulin<\/span>.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Que es paniculitis? Paniculitis es un t\u00e9rmino que generalmente se refiere a un trastorno de la subcut\u00e1neo grasa. \u00bfQu\u00e9 es citof\u00e1gico? histioc\u00edtico paniculitis? La paniculitis histioc\u00edtica citof\u00e1gica es un inflamatorio&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-6667","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/6667","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=6667"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/6667\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=6667"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=6667"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=6667"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}