{"id":7482,"date":"2020-04-24T16:21:09","date_gmt":"2020-04-24T19:21:09","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/telangiectasia-hereditaria-benigna\/"},"modified":"2020-04-27T16:17:33","modified_gmt":"2020-04-27T19:17:33","slug":"telangiectasia-hereditaria-benigna","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/","title":{"rendered":"Benign hereditary telangiectasia"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contents<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#Que-es-telangiectasia\" >What is telangiectasia?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#Que-es-benigno-hereditario-telangiectasia\" >Que es benigno hereditario telangiectasia?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#%C2%BFQue-causa-la-telangiectasia-hereditaria-benigna-y-quien-esta-en-riesgo\" >\u00bfQu\u00e9 causa la telangiectasia hereditaria benigna y qui\u00e9n est\u00e1 en riesgo?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-telangiectasia-hereditaria-benigna\" >\u00bfCu\u00e1les son las caracter\u00edsticas cl\u00ednicas de la telangiectasia hereditaria benigna?<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#Telangiectasia-hereditaria-benigna\" >Benign hereditary telangiectasia<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#%C2%BFComo-se-diagnostica-la-telangiectasia-hereditaria-benigna\" >\u00bfC\u00f3mo se diagnostica la telangiectasia hereditaria benigna?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#%C2%BFCuales-son-los-diagnosticos-diferenciales-para-las-telangiectasias\" >\u00bfCu\u00e1les son los diagn\u00f3sticos diferenciales para las telangiectasias?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-8\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/telangiectasia-hereditaria-benigna\/#%C2%BFCual-es-el-tratamiento-y-el-resultado-de-la-telangiectasia-hereditaria-benigna\" >\u00bfCu\u00e1l es el tratamiento y el resultado de la telangiectasia hereditaria benigna?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Que-es-telangiectasia\"><\/span>What is it <span class=\"term\" data-term-id=\"281\">telangiectasia<\/span>?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>El t\u00e9rmino telangiectasia se refiere a una condici\u00f3n de la piel compuesta de rojo fino <span class=\"term\" data-term-id=\"953\">blood vessels<\/span>: estos se llaman <span class=\"term\" data-term-id=\"700\">telangiectasias<\/span>.<\/p>\n<p><span class=\"term\" data-term-id=\"47\">Cutaneous<\/span> Las telangiectasias son causadas por la dilataci\u00f3n permanente de los vasos sangu\u00edneos peque\u00f1os, lo que resulta en un peque\u00f1o rojo <span class=\"term\" data-term-id=\"321\">linear<\/span> marcas en la piel y <span class=\"term\" data-term-id=\"188\">mucous<\/span> membranas Ellos pueden ser <span class=\"term\" data-term-id=\"949\">primary<\/span> or secondary<\/p>\n<ul>\n<li>Las telangiectasias primarias son causadas por <span class=\"term\" data-term-id=\"862\">idiopathic<\/span> <span class=\"term\" data-term-id=\"756\">capillary<\/span> dilataci\u00f3n (causa desconocida).<\/li>\n<li>Las telangiectasias secundarias se presentan como una caracter\u00edstica de una enfermedad cut\u00e1nea o <span class=\"term\" data-term-id=\"380\">systemic<\/span> proceso de la enfermedad<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"Que-es-benigno-hereditario-telangiectasia\"><\/span>What is it <span class=\"term\" data-term-id=\"22\">benign<\/span> <span class=\"term\" data-term-id=\"1745\">hereditary<\/span> telangiectasia?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La telangiectasia hereditaria benigna es un trastorno telangiect\u00e1sico primario. Tiene diferentes patrones cl\u00ednicos.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-causa-la-telangiectasia-hereditaria-benigna-y-quien-esta-en-riesgo\"><\/span>\u00bfQu\u00e9 causa la telangiectasia hereditaria benigna y qui\u00e9n est\u00e1 en riesgo?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Se desconoce la causa precisa de la telangiectasia hereditaria benigna.<\/p>\n<ul>\n<li>Se hereda en un <span class=\"term\" data-term-id=\"828\">autosomal<\/span> patr\u00f3n dominante Esto significa que se transmite de un padre a aproximadamente la mitad de sus hijos, por lo tanto, varios miembros de la familia pueden verse afectados.<\/li>\n<li>Las telangiectasias tienden a aparecer en los primeros a\u00f1os de vida, a menudo entre las edades de 2 y 12 a\u00f1os. Raramente est\u00e1n presentes al nacer.<\/li>\n<li>Las telangiectasias son a menudo m\u00e1s notadas por las mujeres, pero no se cree que el trastorno sea m\u00e1s com\u00fan en las mujeres.<\/li>\n<li>Las telangiectasias tambi\u00e9n pueden volverse m\u00e1s prominentes durante el embarazo.<\/li>\n<li>A menudo se distribuyen en sitios expuestos a la luz, lo que implica que la luz solar puede desempe\u00f1ar un papel.<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-telangiectasia-hereditaria-benigna\"><\/span>\u00bfCu\u00e1les son las caracter\u00edsticas cl\u00ednicas de la telangiectasia hereditaria benigna?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Las personas con telangiectasias hereditarias benignas tienden a presentar numerosas telangiectasias.<\/p>\n<ul>\n<li>A menudo se distribuyen ampliamente sobre la cara, el cuello, la parte superior del tronco, <span class=\"term\" data-term-id=\"71\">dorsal<\/span>, manos y, con menos frecuencia, rodillas.<\/li>\n<li>Las telangiectasias pueden ser <span class=\"term\" data-term-id=\"1063\">macular<\/span>, <span class=\"term\" data-term-id=\"235\">license plate<\/span>-como, arborising, <span class=\"term\" data-term-id=\"1343\">lattice<\/span>, puntiagudo, moteado, parecido a una ara\u00f1a y lineal.<\/li>\n<li>Las telangiectasias punteadas pueden estar rodeadas de halos p\u00e1lidos (fen\u00f3meno de robo).<\/li>\n<li>Algunas lesiones pueden ser indistinguibles de la ara\u00f1a. <span class=\"term\" data-term-id=\"699\">telangiectasia<\/span>.<\/li>\n<li>Las telangiectasias tempranas pueden ser peque\u00f1as y <span class=\"term\" data-term-id=\"967\">erythematous<\/span>. A menudo aumentan de tama\u00f1o y pueden volverse m\u00e1s p\u00e1lidos con la edad.<\/li>\n<li>the <span class=\"term\" data-term-id=\"1018\">mucous membrane<\/span> las membranas no se ven afectadas con la excepci\u00f3n del borde bermell\u00f3n de los labios.<\/li>\n<li>No hay afectaci\u00f3n sist\u00e9mica o sangrado, en contraste con la enfermedad hereditaria. <span class=\"term\" data-term-id=\"121\">hemorrhagic<\/span> telangiectasia<\/li>\n<li>Las telangiectasias son invariablemente <span class=\"term\" data-term-id=\"731\">asymptomatic<\/span> y causa solo una leve preocupaci\u00f3n cosm\u00e9tica.<\/li>\n<\/ul>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Telangiectasia-hereditaria-benigna\"><\/span>Benign hereditary telangiectasia<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-01__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-8476400-4505077' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-01__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-8476400.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-02__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-7020435-5512727' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-02__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-7020435.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-03__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-4792554-4692053' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-03__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-4792554.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-04__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-9670730-4680681' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-04__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-9670730.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-05__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-8588208-8005038' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-05__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-8588208.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-06__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-2784874-8019206' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-06__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-2784874.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-07__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-8945659-4456677' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-07__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-8945659.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='benign-telangiectasia-08__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-6298846-1507825' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/benign-telangiectasia-08__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-6298846.jpg'>\n<\/div>\n<p class=\"p-small\">Benign hereditary telangiectasia<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-diagnostica-la-telangiectasia-hereditaria-benigna\"><\/span>\u00bfC\u00f3mo se diagnostica la telangiectasia hereditaria benigna?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La telangiectasia hereditaria benigna es un diagn\u00f3stico cl\u00ednico. <span class=\"term\" data-term-id=\"474\">Histological<\/span> El examen de la piel lesional muestra dilataci\u00f3n del subpapilar <span class=\"term\" data-term-id=\"1178\">venous<\/span> plexo con la parte superior asociada <span class=\"term\" data-term-id=\"52\">dermal<\/span> <span class=\"term\" data-term-id=\"18\">atrophy<\/span>.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-los-diagnosticos-diferenciales-para-las-telangiectasias\"><\/span>\u00bfCu\u00e1les son los diagn\u00f3sticos diferenciales para las telangiectasias?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La condici\u00f3n m\u00e1s importante para descartar es la telangiectasia hemorr\u00e1gica hereditaria (Osler-Rendu-Weber <span class=\"term\" data-term-id=\"350\">syndrome<\/span>) Los diagn\u00f3sticos diferenciales de telangiectasias primarias en ni\u00f1os tambi\u00e9n incluyen:<\/p>\n<ul>\n<li>Spider telangiectasia<\/li>\n<li>  Ataxia-telangiectasia <\/li>\n<li><span class=\"term\" data-term-id=\"308\">Generalized<\/span> essential telangiectasia<\/li>\n<li>\n<span class=\"term\" data-term-id=\"292\">Unilateral<\/span> telangiectasia nevoide<\/li>\n<li> <span class=\"term\" data-term-id=\"358\">Angioma<\/span> serpiginous <\/li>\n<li>Capillary <span class=\"term\" data-term-id=\"753\">vascular<\/span> malformations<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-el-tratamiento-y-el-resultado-de-la-telangiectasia-hereditaria-benigna\"><\/span>\u00bfCu\u00e1l es el tratamiento y el resultado de la telangiectasia hereditaria benigna?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Debido a la falta de compromiso sist\u00e9mico, la telangiectasia hereditaria benigna tiene una excelente <span class=\"term\" data-term-id=\"241\">forecast<\/span> y generalmente no se requiere intervenci\u00f3n m\u00e9dica.<\/p>\n<p>Cuando se solicita tratamiento por razones est\u00e9ticas, se pueden considerar los siguientes tratamientos.<\/p>\n<ul>\n<li>Sclerotherapy<\/li>\n<li>  Intense pulsed light <\/li>\n<li>Vascular <span class=\"term\" data-term-id=\"1617\">To be<\/span> <\/li>\n<li>  Electrosurgery <\/li>\n<\/ul>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Que es telangiectasia? El t\u00e9rmino telangiectasia se refiere a una condici\u00f3n de la piel compuesta de rojo fino vasos sanguineos: estos se llaman telangiectasias. Cut\u00e1neo Las telangiectasias son causadas por&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-7482","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/7482","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=7482"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/7482\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=7482"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=7482"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=7482"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}