{"id":7532,"date":"2020-04-24T21:20:21","date_gmt":"2020-04-25T00:20:21","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/malformacion-venosa\/"},"modified":"2020-04-27T16:09:52","modified_gmt":"2020-04-27T19:09:52","slug":"venous-malformation","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/","title":{"rendered":"Venous malformation"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contents<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#Que-son-venoso-malformaciones\" >What are venous malformations?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#Glomuvenous-malformacion\" >Glomuvenous malformation<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#Malformacion-arteriovenosa\" >arteriovenous malformation<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#Bleb-de-goma-azul-nevus-sindrome\" >Blue Gum Bleb Nevus Syndrome<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#Sindrome-de-nevo-de-ampolla-de-goma-azul\" >Blue rubber blister nevus syndrome<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#Sindrome-de-maffucci\" >maffucci syndrome<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#%C2%BFQue-investigaciones-deberian-hacerse\" >What research should be done?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-8\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/malformacion-venosa\/#Tratamiento-de-malformaciones-venosas\" >Treatment of venous malformations.<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Que-son-venoso-malformaciones\"><\/span>What are they <span class=\"term\" data-term-id=\"1178\">venous<\/span> malformations?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Venous malformations are a type of <span class=\"term\" data-term-id=\"753\">vascular<\/span> <span class=\"term\" data-term-id=\"353\">nevus<\/span> or birthmark. They are due to malformed dilated veins and are not cancerous. They appear as skin-colored, blue, or purple swellings anywhere on the body, and there are often prominent veins near the surface of the skin. I like it <span class=\"term\" data-term-id=\"756\">capillary<\/span> vascular malformations (port-wine stains), venous malformations are always present at birth, although they may become more apparent over time. They can range in size from a small spot to occasionally involving an entire limb. Unlike cavernous <span class=\"term\" data-term-id=\"361\">hemangiomas<\/span>, grow in proportion to the overall growth of the child.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Glomuvenous-malformacion\"><\/span>Glomuvenous <span class=\"term\" data-term-id=\"1631\">malformation<\/span><br \/>\n<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Glomuvenous malformation is also known as glomangioma or glomangiomatosis. These differ from standard venous malformations by being multiple in appearance, slightly raised, blue or bluish-purple in color. There are characteristic features of this <span class=\"term\" data-term-id=\"164\">injury<\/span> on the skin <span class=\"term\" data-term-id=\"24\">biopsy<\/span> (<span class=\"term\" data-term-id=\"128\">histology<\/span>) Glomuveous malformations can be inherited as a <span class=\"term\" data-term-id=\"828\">autosomal<\/span> dominant trait, which means that half of the children of an affected person will have a tendency to develop these lesions to a variable degree. They are due to a <span class=\"term\" data-term-id=\"870\">mutation<\/span> in the glomulin <span class=\"term\" data-term-id=\"774\">gene<\/span>.<\/p>\n<p>Glomuveous malformations must be distinguished from glomus solitary tumors, which usually occur under or next to a nail in an adult, and are not inherited. They are small, but exquisitely tender blue or purple. <span class=\"term\" data-term-id=\"367\">nodules<\/span> with a fibrous border An x-ray may show underlying <span class=\"term\" data-term-id=\"535\">erosion<\/span> of the bone Tumors of the glomus solitarius are due to a <span class=\"term\" data-term-id=\"893\">proliferation<\/span> of glomus cells; The diagnosis is confirmed by skin biopsy.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Malformacion-arteriovenosa\"><\/span>\n<p>arteriovenous malformation<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>An arteriovenous malformation refers to the communication between an artery and a vein. The affected skin feels warmer than the surrounding skin. It is possible to feel a &quot;thrill&quot; due to the high flow of blood through the arteriovenous malformation. The doctor listening with a stethoscope may hear a roar or &quot;murmur.&quot; These are sometimes associated with other abnormalities in various vascular syndromes.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Bleb-de-goma-azul-nevus-sindrome\"><\/span>Blue rubber bleb nevus <span class=\"term\" data-term-id=\"350\">syndrome<\/span><br \/>\n<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Blue rubber bleb nevus syndrome or Bean syndrome is a rare form of venous malformation in which there are lesions in the skin and gastrointestinal tract. There is often a family history, with <span class=\"term\" data-term-id=\"829\">autosomal dominant<\/span> inheritance, that is, the tendency to the syndrome is transmitted to half of the children.<\/p>\n<p>Skin lesions present as blue or purple compressible rubbery nodules with a wrinkled surface. There may be a single injury or hundreds of injuries throughout the body. Lesions in the gastrointestinal tract (mouth to rectum) can bleed and cause <span class=\"term\" data-term-id=\"598\">anemia<\/span> or rarely, sudden death. The nodules remain unchanged for life.<\/p>\n<p>Surgical <span class=\"term\" data-term-id=\"848\">excision<\/span>, sclerotherapy and\/or <span class=\"term\" data-term-id=\"1617\">To be<\/span> Therapy may be indicated. However, in most cases no treatment is required.<\/p>\n<p>A case history has described marked improvement after oral sirolimus (which inhibits <span class=\"term\" data-term-id=\"1404\">angiogenesis<\/span>) This drug is being investigated as a possible medical treatment for serious vascular malformations, but may have significant side effects.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Sindrome-de-nevo-de-ampolla-de-goma-azul\"><\/span>Blue rubber blister nevus syndrome<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='brbn1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-7347168-7861388' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/brbn1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-7347168.jpg'>\n<\/div>\n<p class=\"p-small\">Blue rubber bleb nevus<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='brbn2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-3579325-6930231' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/brbn2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-3579325.jpg'>\n<\/div>\n<p class=\"p-small\">Blue rubber bleb nevus<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='brbn3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-4117833-4772977' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/brbn3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-4117833.jpg'>\n<\/div>\n<p class=\"p-small\">Blue rubber bleb nevus<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Sindrome-de-maffucci\"><\/span>\n<p>maffucci syndrome<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Maffucci syndrome is a rare <span class=\"term\" data-term-id=\"558\">genetic<\/span> disorder that affects both men and women. It is characterized by cartilage growths (enchondromas), bone deformities and venous malformations. The disease is present at birth or develops during childhood.<\/p>\n<p>Venous malformations stand out as soft blue nodules on the arms and legs or elsewhere. Enchondromas are often found in the fingers, toes, or the ends of long bones. Sometimes they result in fractures. <span class=\"term\" data-term-id=\"30\">Cancer<\/span> (chondrosarcoma) can arise within enchondromas in approximately 30% of adult patients.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-investigaciones-deberian-hacerse\"><\/span>What research should be done?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Venous malformations are usually diagnosed clinically. However, a <span class=\"term\" data-term-id=\"1378\">ultrasound<\/span> The scan is often done to find out the extent of the abnormality. Characteristically, a compressible tubular venous malformation shows <span class=\"term\" data-term-id=\"953\">blood vessels<\/span>. In some cases, fresh or older calcified blood clots (<span class=\"term\" data-term-id=\"769\">thrombosis<\/span>) can be detected.<\/p>\n<p>Ultrasound evaluation of arteriovenous malformations also shows evidence of blood shunting between the affected artery and vein with turbulent blood flow.<\/p>\n<p>In more complicated cases it may be necessary to perform <span class=\"term\" data-term-id=\"1410\">Magnetic resonance imaging<\/span> (<span class=\"term\" data-term-id=\"1116\">Magnetic resonance<\/span>) or <span class=\"term\" data-term-id=\"1369\">angiography<\/span> to help plan treatment.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Tratamiento-de-malformaciones-venosas\"><\/span>Treatment of venous malformations.<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Treatment of venous malformations is very difficult and often involves complex surgery and\/or ultrasound-guided sclerotherapy. Vascular lasers may be helpful in some cases.<\/p>\n<p>Extensive malformations require careful evaluation, often by a team of specialists that may include a <span class=\"term\" data-term-id=\"919\">pediatric<\/span> <span class=\"term\" data-term-id=\"54\">dermatologist<\/span>, pediatrician, radiologist, plastic surgeon and\/or vascular surgeon.<\/p>\n<p>General care may include pain relief and compression therapy.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Qu\u00e9 son venoso malformaciones? Las malformaciones venosas son un tipo de vascular nevo o marca de nacimiento. Se deben a venas dilatadas malformadas y no son cancerosas. Aparecen como hinchazones&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-7532","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/7532","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=7532"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/7532\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=7532"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=7532"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=7532"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}