{"id":7737,"date":"2020-04-25T16:20:28","date_gmt":"2020-04-25T19:20:28","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/patologia-del-fibroblastoma-desmoplasico\/"},"modified":"2020-04-30T21:34:19","modified_gmt":"2020-05-01T00:34:19","slug":"patologia-del-fibroblastoma-desmoplasico","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-fibroblastoma-desmoplasico\/","title":{"rendered":"Pathology of desmoplastic fibroblastoma"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contents<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-fibroblastoma-desmoplasico\/#Introduccion\" >Introduction<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-fibroblastoma-desmoplasico\/#Histologia-del-fibroblastoma-desmoplasico\" >Histolog\u00eda del fibroblastoma desmopl\u00e1sico<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-fibroblastoma-desmoplasico\/#Patologia-del-fibroblastoma-desmoplasico\" >Pathology of desmoplastic fibroblastoma<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-fibroblastoma-desmoplasico\/#Estudios-especiales-para-fibroblastoma-desmoplasico\" >Estudios especiales para fibroblastoma desmopl\u00e1sico<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/patologia-del-fibroblastoma-desmoplasico\/#Diagnostico-diferencial-del-fibroblastoma-desmoplasico\" >Diagn\u00f3stico diferencial del fibroblastoma desmopl\u00e1sico<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Introduccion\"><\/span>Introduction<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>De otra manera conocido como <span class=\"term\" data-term-id=\"1185\">collagen<\/span> <span class=\"term\" data-term-id=\"337\">fibroma<\/span>, <span class=\"term\" data-term-id=\"1662\">desmoplastic<\/span> El fibroblastoma es un <span class=\"term\" data-term-id=\"22\">benign<\/span> <span class=\"term\" data-term-id=\"289\">tumor<\/span> que se presenta como masas de crecimiento lento en el <span class=\"term\" data-term-id=\"1282\">subcutis<\/span> y ocurren principalmente en la mediana edad. Se han descrito involucrando una amplia gama de sitios anat\u00f3micos, pero generalmente surgen en la extremidad superior.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Histologia-del-fibroblastoma-desmoplasico\"><\/span>\n<span class=\"term\" data-term-id=\"128\">Histology<\/span> del fibroblastoma desmopl\u00e1sico<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Las secciones de fibroblastoma desmopl\u00e1sico muestran un relativamente buen<span class=\"term\" data-term-id=\"37\">circumscribed<\/span> tumor en <span class=\"term\" data-term-id=\"900\">subcutaneous<\/span> tejido adiposo (figura 1). El tumor est\u00e1 compuesto de fibroso o ligeramente <span class=\"term\" data-term-id=\"191\">myxoid<\/span> <span class=\"term\" data-term-id=\"43\">connective tissue<\/span> con escasas c\u00e9lulas spindled intercaladas (figura 2). Los vasos no son visibles, pero pueden mostrar <span class=\"term\" data-term-id=\"228\">perivascular<\/span> <span class=\"term\" data-term-id=\"260\">sclerosis<\/span>. Alto aumento muestra el <span class=\"term\" data-term-id=\"1660\">spindle cells<\/span> son sosos, con algunos <span class=\"term\" data-term-id=\"237\">polygonal<\/span> formas (figura 3). <span class=\"term\" data-term-id=\"1535\">Mitosis<\/span> est\u00e1n ausentes o extremadamente escasos.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Patologia-del-fibroblastoma-desmoplasico\"><\/span>Pathology of desmoplastic fibroblastoma<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='desmoplastic-fibroblastoma-figure-1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisinkildezxq-1635152-4567818' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/desmoplastic-fibroblastoma-figure-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDEzXQ-1635152.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='desmoplastic-fibroblastoma-figure-2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-4174699-9236639' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/desmoplastic-fibroblastoma-figure-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-4174699.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='desmoplastic-fibroblastoma-figure-3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-9058901-3592065' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/desmoplastic-fibroblastoma-figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-9058901.jpg'>\n<\/div>\n<p class=\"p-small\">figure 3<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Estudios-especiales-para-fibroblastoma-desmoplasico\"><\/span>Estudios especiales para fibroblastoma desmopl\u00e1sico<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Los estudios inmunohistoqu\u00edmicos revelan que el fibroblastoma desmopl\u00e1sico es negativo con S100, CD34, desmina.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Diagnostico-diferencial-del-fibroblastoma-desmoplasico\"><\/span>\n<span class=\"term\" data-term-id=\"813\">Differential diagnosis<\/span> del fibroblastoma desmopl\u00e1sico<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span class=\"term\" data-term-id=\"875\">Neurofibroma<\/span> &#8211; estos pueden tener una matriz de fibromixoide similar pero las c\u00e9lulas son onduladas y est\u00e1n m\u00e1s densamente empaquetadas. S100 ser\u00e1 fuertemente positivo en neurofibroma.<\/p>\n<p>Low-grade fibromyxoid <span class=\"term\" data-term-id=\"1665\">sarcoma<\/span> &#8211; estos son m\u00e1s <span class=\"term\" data-term-id=\"956\">cellular<\/span> y las celdas a menudo est\u00e1n dispuestas en un patr\u00f3n en espiral.<\/p>\n<p><span class=\"term\" data-term-id=\"52\">Dermal<\/span> <span class=\"term\" data-term-id=\"1191\">scar<\/span> &#8211; estos generalmente no est\u00e1n tan bien circunscritos y pueden mostrar <span class=\"term\" data-term-id=\"490\">inflammatory<\/span> cambios, <span class=\"term\" data-term-id=\"112\">granulation tissue<\/span> u otros cambios reactivos dependiendo de la etapa de la cicatriz<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Introducci\u00f3n De otra manera conocido como col\u00e1geno fibroma, desmopl\u00e1stico El fibroblastoma es un benigno tumor que se presenta como masas de crecimiento lento en el subcutis y ocurren principalmente en&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[205],"class_list":["post-7737","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones","tag-patologia"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/7737","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=7737"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/7737\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=7737"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=7737"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=7737"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}