{"id":8006,"date":"2020-04-26T18:51:11","date_gmt":"2020-04-26T21:51:11","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/elastosis-perforante-serpiginosa\/"},"modified":"2020-04-27T14:58:39","modified_gmt":"2020-04-27T17:58:39","slug":"elastosis-perforante-serpiginosa","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/","title":{"rendered":"Serpiginous perforating elastosis"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contents<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/#Que-es-elastosis-perforans-serpiginosa\" >Que es elastosis perforans serpiginosa?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/#%C2%BFQuien-contrae-elastosis-perforante-serpiginosa\" >\u00bfQui\u00e9n contrae elastosis perforante serpiginosa?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/#%C2%BFQue-causa-la-elastosis-perforante-serpiginosa\" >\u00bfQu\u00e9 causa la elastosis perforante serpiginosa?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/#%C2%BFCuales-son-los-signos-y-sintomas-de-la-elastosis-perforante-serpiginosa\" >\u00bfCu\u00e1les son los signos y s\u00edntomas de la elastosis perforante serpiginosa?<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/#Elastosis-perforante-serpiginosa\" >Serpiginous perforating elastosis<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/#%C2%BFComo-se-hace-el-diagnostico-de-elastosis-perforante-serpiginosa\" >\u00bfC\u00f3mo se hace el diagn\u00f3stico de elastosis perforante serpiginosa?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/elastosis-perforante-serpiginosa\/#%C2%BFQue-tratamiento-hay-disponible-para-la-elastosis-perforante-serpiginosa\" >\u00bfQu\u00e9 tratamiento hay disponible para la elastosis perforante serpiginosa?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Que-es-elastosis-perforans-serpiginosa\"><\/span>What is it <span class=\"term\" data-term-id=\"80\">elastosis<\/span> perforans serpiginosa?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La elastosis perforante serpiginosa (EPS) es un trastorno cut\u00e1neo raro en el que la fibra anormal de tejido el\u00e1stico pasa de la papila <span class=\"term\" data-term-id=\"61\">dermis<\/span> (capa interna de piel) a la <span class=\"term\" data-term-id=\"85\">epidermis<\/span> (capa externa de la piel), descrita como eliminaci\u00f3n transepitelial. Se presenta como un grupo de peque\u00f1as protuberancias rojizas.<\/p>\n<p>Tres formas de <span>elastosis perforante serpiginosa<\/span> han sido identificados:<\/p>\n<ul>\n<li>\n<span class=\"term\" data-term-id=\"862\">Idiopathic<\/span> <span>elastosis perforante serpiginosa<\/span>: origen desconocido, posiblemente <span class=\"term\" data-term-id=\"558\">genetic<\/span>\n<\/li>\n<li>Reactivo <span>elastosis perforante serpiginosa<\/span>: asociado con otros trastornos hereditarios como Down <span class=\"term\" data-term-id=\"350\">syndrome<\/span>, S\u00edndrome de Ehlers Danlos y s\u00edndrome de Marfan\n<\/li>\n<li>Drug induced <span>elastosis perforante serpiginosa<\/span>: afecta al 1% de las personas tratadas con D-penicilamina<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQuien-contrae-elastosis-perforante-serpiginosa\"><\/span>\u00bfQui\u00e9n contrae elastosis perforante serpiginosa?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span>Serpiginous perforating elastosis<\/span> aparece m\u00e1s com\u00fanmente durante la edad adulta temprana (20-30 a\u00f1os) pero puede verse en la primera infancia o en la vejez. Parece ser m\u00e1s com\u00fan en hombres que en mujeres (proporci\u00f3n 4: 1).<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-causa-la-elastosis-perforante-serpiginosa\"><\/span>\u00bfQu\u00e9 causa la elastosis perforante serpiginosa?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span>Serpiginous perforating elastosis<\/span> ocurre porque la epidermis (la capa externa de la piel) percibe que el tejido el\u00e1stico anormal es un objeto extra\u00f1o, respondiendo as\u00ed a trav\u00e9s de un <span class=\"term\" data-term-id=\"490\">inflammatory<\/span> ataque. Se desconoce la causa del tejido el\u00e1stico anormal, pero puede ser de origen gen\u00e9tico. <span class=\"term\" data-term-id=\"870\">mutation<\/span> o factores externos como la penicilamina.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-los-signos-y-sintomas-de-la-elastosis-perforante-serpiginosa\"><\/span>\u00bfCu\u00e1les son los signos y s\u00edntomas de la elastosis perforante serpiginosa?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span>Serpiginous perforating elastosis<\/span> se presenta como un grupo de peque\u00f1as protuberancias rojizas de 2-5 mm de di\u00e1metro, a menudo <span class=\"term\" data-term-id=\"116\">grouped<\/span> in <span class=\"term\" data-term-id=\"321\">linear<\/span>circular o <span class=\"term\" data-term-id=\"265\">serpiginous<\/span> (como serpientes) patrones. Cada <span class=\"term\" data-term-id=\"164\">injury<\/span> puede tener un hoyo central, que a veces se llena con una costra <span class=\"term\" data-term-id=\"385\">scaly<\/span> enchufe. Por lo general, no hay s\u00edntomas, pero a veces <span>elastosis perforante serpiginosa<\/span> tiene picaz\u00f3n<\/p>\n<p><span>Serpiginous perforating elastosis<\/span> generalmente surge en la parte posterior del cuello (70%) y con menos frecuencia en uno o ambos brazos (20%), cara (11%), piernas (6%) y tronco (3%).<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Elastosis-perforante-serpiginosa\"><\/span>Serpiginous perforating elastosis<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='eps1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildi2xq-7664240-2597622' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/eps1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDI2XQ-7664240.jpg'>\n<\/div>\n<p class=\"p-small\">Serpiginous perforating elastosis<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='eps2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildhd-5490859-7450753' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/eps2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDhd-5490859.jpg'>\n<\/div>\n<p class=\"p-small\">Serpiginous perforating elastosis<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='eps3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisinkildmzxq-7691211-3660622' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/eps3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDMzXQ-7691211.jpg'>\n<\/div>\n<p class=\"p-small\">Serpiginous perforating elastosis<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-hace-el-diagnostico-de-elastosis-perforante-serpiginosa\"><\/span>\u00bfC\u00f3mo se hace el diagn\u00f3stico de elastosis perforante serpiginosa?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>El diagn\u00f3stico de elastosis perforante serpiginosa se realiza por su aspecto cl\u00ednico y por la caracter\u00edstica <span class=\"term\" data-term-id=\"128\">histology<\/span> of <span>elastosis perforante serpiginosa<\/span> seen on the skin <span class=\"term\" data-term-id=\"24\">biopsy<\/span>mostrando <span class=\"term\" data-term-id=\"287\">transepidermal<\/span> eliminaci\u00f3n de tejido el\u00e1stico (y no elastosis).<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-tratamiento-hay-disponible-para-la-elastosis-perforante-serpiginosa\"><\/span>\u00bfQu\u00e9 tratamiento hay disponible para la elastosis perforante serpiginosa?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>No hay cura para <span>elastosis perforante serpiginosa<\/span>. Por lo general, se resuelve espont\u00e1neamente sin complicaciones despu\u00e9s de unos a\u00f1os.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Que es elastosis perforans serpiginosa? La elastosis perforante serpiginosa (EPS) es un trastorno cut\u00e1neo raro en el que la fibra anormal de tejido el\u00e1stico pasa de la papila dermis (capa&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-8006","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/8006","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=8006"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/8006\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=8006"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=8006"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=8006"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}