<\/span><\/h2>\nFamily<\/span> benign<\/span> El p\u00e9nfigo, tambi\u00e9n llamado enfermedad de Hailey-Hailey, es una enfermedad ampollosa causada por mutations<\/span> en el ATP2C1 gene<\/span>, with autosomal<\/span>-la herencia dominante. El gen ATP2C1 es vital para keratinocytes<\/span> accession<\/span> and differentiation<\/span>. Por lo general, la presentaci\u00f3n cl\u00ednica comienza durante la segunda o tercera d\u00e9cada. Las principales \u00e1reas afectadas son los pliegues de la piel, con humedad. cracked<\/span> maloliente plates<\/span> y ampollas El curso de la enfermedad es variable y el tratamiento es principalmente sintom\u00e1tico.<\/p>\n<\/span>\nHistology<\/span> de p\u00e9nfigo familiar benigno<\/span><\/h2>\nEn el p\u00e9nfigo familiar benigno, acantholysis<\/span> afecta a todo epidermis<\/span>, dando la descripci\u00f3n cl\u00e1sica de la pared de ladrillo en ruinas (figuras 1\u20134). los hair<\/span> follicles<\/span> generalmente se salvan, t\u00edpicamente, con acanthosis<\/span> and dyskeratosis<\/span>.<\/p>\n\n<\/span>Patolog\u00eda de la enfermedad de Hailey Hailey<\/span><\/h5>\n<\/section>\n\n\n
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Figure 1<\/p>\n
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Figure 2<\/p>\n
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figure 3<\/p>\n
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Figure 4<\/p>\n<\/p><\/div>\n<\/section>\n
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<\/span>Estudios especiales para el p\u00e9nfigo familiar benigno<\/span><\/h2>\nDirect immunofluorescence<\/span> se aplica al tejido fresco para excluir una enfermedad inmunobulosa, particularmente el p\u00e9nfigo vulgar.<\/p>\n<\/span>\nDifferential diagnosis<\/span> de p\u00e9nfigo familiar benigno<\/span><\/h2>\nEnfermedad de Grover: generalmente m\u00e1s focal<\/span> histologically<\/span>.<\/p>\nP\u00e9nfigo vulgar: inmunofluorescencia directa positiva y es m\u00e1s probable que afecte los fol\u00edculos capilares.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"
Introducci\u00f3n Familiar benigno El p\u00e9nfigo, tambi\u00e9n llamado enfermedad de Hailey-Hailey, es una enfermedad ampollosa causada por mutaciones en el ATP2C1 gene, con autos\u00f3mico-la herencia dominante. El gen ATP2C1 es vital…<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[205],"class_list":["post-8140","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones","tag-patologia"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/8140","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=8140"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/8140\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=8140"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=8140"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=8140"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}