{"id":8153,"date":"2020-04-27T09:33:07","date_gmt":"2020-04-27T12:33:07","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/fibromatosis\/"},"modified":"2020-04-27T14:13:55","modified_gmt":"2020-04-27T17:13:55","slug":"fibromatosis","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/en\/wiki\/fibromatosis\/","title":{"rendered":"Fibromatosis"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contents<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/fibromatosis\/#%C2%BFQue-es-la-fibromatosis\" >What is fibromatosis?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/fibromatosis\/#%C2%BFCual-es-la-clasificacion-de-la-fibromatosis\" >What is the classification of fibromatosis?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/fibromatosis\/#%C2%BFCuales-son-las-caracteristicas-de-la-fibromatosis\" >What are the characteristics of fibromatosis?<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/fibromatosis\/#Fibromatosis\" >Fibromatosis<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/fibromatosis\/#%C2%BFQue-causa-la-fibromatosis\" >What causes fibromatosis?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/doctorhoogstra.com\/en\/wiki\/fibromatosis\/#%C2%BFCual-es-el-tratamiento-para-la-fibromatosis\" >What is the treatment for fibromatosis?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-es-la-fibromatosis\"><\/span>What is fibromatosis?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Fibromatosis is a condition where the fibrous growth of <span class=\"term\" data-term-id=\"52\">dermal<\/span> and <span class=\"term\" data-term-id=\"900\">subcutaneous<\/span> <span class=\"term\" data-term-id=\"43\">connective tissue<\/span> develop tumors called <span class=\"term\" data-term-id=\"338\">fibroids<\/span>. These fibroids are generally <span class=\"term\" data-term-id=\"22\">benign<\/span> (not cancerous).<\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-la-clasificacion-de-la-fibromatosis\"><\/span>What is the classification of fibromatosis?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>There seem to be many different ways to classify fibromatosis. A classification system used is based on age (i.e. <span class=\"term\" data-term-id=\"1610\">youth<\/span> vs. adult fibromatosis) and location (i.e. superficial vs. deep fibromatosis).<\/p>\n<table class=\"borders\">\n<tbody>\n<tr>\n<th>Youth<\/th>\n<th>Adult<\/th>\n<\/tr>\n<tr>\n<td rowspan=\"2\">\n<ul>\n<li>\n<span class=\"term\" data-term-id=\"1036\">Congenital<\/span> <span class=\"term\" data-term-id=\"308\">generalized<\/span> fibromatosis (childhood myofibromatosis)<\/li>\n<li>Aponeurotic <span class=\"term\" data-term-id=\"337\">fibroma<\/span>\n<\/li>\n<li>Childhood digital fibromatosis<\/li>\n<li>Aggressive childhood fibromatosis<\/li>\n<li>Fibromatosis colli<\/li>\n<li>Lenticular dermatofibrosis (Buschke-Ollendorf <span class=\"term\" data-term-id=\"350\">syndrome<\/span>)<\/li>\n<\/ul>\n<\/td>\n<td>Superficial fibromatosis (fascial)<\/p>\n<ul>\n<li>\n<span class=\"term\" data-term-id=\"585\">Palm<\/span> (Dupuytren <span class=\"term\" data-term-id=\"1757\">contracture<\/span>) and <span class=\"term\" data-term-id=\"588\">plant<\/span> (Ledderhose disease) fibromatosis<\/li>\n<li>Pachydermodactyly<\/li>\n<li>Fibromatosis of the penis (Peyronie&#039;s disease)<\/li>\n<li>Knuckles<\/li>\n<li>Dermatofibroma<\/li>\n<li>\n<span class=\"term\" data-term-id=\"733\">Nodular<\/span> fasciitis<\/li>\n<li>Elastofibroma<\/li>\n<li>Fibrous <span class=\"term\" data-term-id=\"217\">papule<\/span> Of the face<\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<tr>\n<td>Deep fibromatosis (musculoaponeurotic)<\/p>\n<ul>\n<li>Desmoid tumors (aggressive fibromatosis)\n<ul>\n<li>Extra-abdominal fibromatosis<\/li>\n<li>Abdominal fibromatosis<\/li>\n<li>Intra-abdominal fibromatosis (eg, pelvic fibromatosis)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>See also elastofibroma. <span class=\"term\" data-term-id=\"223\">pathology<\/span>.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-las-caracteristicas-de-la-fibromatosis\"><\/span>What are the characteristics of fibromatosis?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>The following table lists the distinctive features between deep and superficial fibromatosis.<\/p>\n<table class=\"borders\">\n<tbody>\n<tr>\n<th>Superficial fibromatosis<\/th>\n<th>Deep fibromatosis<\/th>\n<\/tr>\n<tr>\n<td>\n<ul>\n<li>Slow growth <span class=\"term\" data-term-id=\"289\">tumor<\/span>\n<\/li>\n<li>Small size<\/li>\n<li>Arise from <span class=\"term\" data-term-id=\"1761\">fascia<\/span> or fascia<\/li>\n<li>Less aggressive<\/li>\n<\/ul>\n<\/td>\n<td>\n<ul>\n<li>Rapidly growing pseudotumor<\/li>\n<li>They usually reach a large size<\/li>\n<li>Often involve deeper structures (trunk and limb muscles)<\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>While most fibromatosis are benign tumors and are not <span class=\"term\" data-term-id=\"1067\">metastasis<\/span> (they spread to other parts of the body), desmoid tumors although they do not metastasize like <span class=\"term\" data-term-id=\"176\">evil one<\/span> cancers can be locally aggressive. They can grow rapidly in large tumors that can obstruct vital structures such as major <span class=\"term\" data-term-id=\"953\">blood vessels<\/span>, <span class=\"term\" data-term-id=\"952\">nerves<\/span> and organs.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Fibromatosis\"><\/span>Fibromatosis<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='inf-fibroma__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildiwxq-3764275-5106097' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/inf-fibroma__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDIwXQ-3764275.jpg'>\n<\/div>\n<p class=\"p-small\">Children&#039;s digital fibroma<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='knuckle1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-7789482-9315946' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/knuckle1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-7789482.jpg'>\n<\/div>\n<p class=\"p-small\">Knuckles<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='dermfib1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisinkildzd-2535856-2128126' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/dermfib1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDZd-2535856.jpg'>\n<\/div>\n<p class=\"p-small\">Dermatofibroma<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='fibrous-papule__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-8660775-6959536' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/fibrous-papule__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-8660775.jpg'>\n<\/div>\n<p class=\"p-small\">Fibrous papule<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='tubscler3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisinkildg1xq-8606435-7388842' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/tubscler3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDg1XQ-8606435.jpg'>\n<\/div>\n<p class=\"p-small\">Periungual fibroma<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-causa-la-fibromatosis\"><\/span>What causes fibromatosis?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>The cause of fibromatosis remains unclear. In some types of fibromatosis, such as desmoid tumors, it is believed that the condition may be related to <span class=\"term\" data-term-id=\"1365\">trauma<\/span>, hormonal factors, or having a <span class=\"term\" data-term-id=\"558\">genetic<\/span> association. Superficial fibromatosis such as palmar, plantar, and penile fibromatosis have sometimes been linked to certain diseases such as diabetes, liver disease, and <span class=\"term\" data-term-id=\"561\">hypertension<\/span>.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-el-tratamiento-para-la-fibromatosis\"><\/span>What is the treatment for fibromatosis?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>The management of fibromatosis depends on the individual disease. For more information on the different types of fibromatosis, select from the list below.<\/p>\n<ul>\n<li>\n<p>Generalized congenital fibromatosis (childhood myofibromatosis)<\/li>\n<li>Aponeurotic fibroma<\/li>\n<li>Childhood digital fibromatosis<\/li>\n<li>Aggressive childhood fibromatosis<\/li>\n<li>Fibromatosis colli<\/li>\n<li>Lenticular dermatofibrosis (Buschke-Ollendorf syndrome)<\/li>\n<li>Palmar (Dupuytren&#039;s disease) and plantar fibromatosis (Ledderhose&#039;s disease)<\/li>\n<li>Fibromatosis of the penis (Peyronie&#039;s disease)<\/li>\n<li>Knuckles<\/li>\n<li>Pachydermodactyly<\/li>\n<li>Dermatofibroma<\/li>\n<li>Nodular fasciitis<\/li>\n<li>Elastofibroma<\/li>\n<li>Fibrous papule of the nose or face<\/li>\n<li>Desmoid tumors (aggressive fibromatosis)<\/li>\n<\/ul>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>\u00bfQu\u00e9 es la fibromatosis? La fibromatosis es una condici\u00f3n donde el crecimiento fibroso de d\u00e9rmico y subcut\u00e1neo tejido conectivo desarrollar tumores llamados fibromas. Estos fibromas son generalmente benigno (no canceroso)&#8230;.<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-8153","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/8153","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/comments?post=8153"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/wiki\/8153\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/media?parent=8153"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/categories?post=8153"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/en\/wp-json\/wp\/v2\/tags?post=8153"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}