{"id":16498,"date":"2020-04-28T13:23:40","date_gmt":"2020-04-28T16:23:40","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/wiki\/patologia-tumoral-miofibroblastica-inflamatoria\/"},"modified":"2020-04-30T21:34:05","modified_gmt":"2020-05-01T00:34:05","slug":"pathologie-tumeur-myofibroblastique-inflammatoire","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/fr\/wiki\/patologia-tumoral-miofibroblastica-inflamatoria\/","title":{"rendered":"Pathologie tumorale myofibroblastique inflammatoire"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contenu<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Basculer la table des mati\u00e8res\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Basculer<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/patologia-tumoral-miofibroblastica-inflamatoria\/#Introduccion\" >introduction<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/patologia-tumoral-miofibroblastica-inflamatoria\/#Histologia-del-tumor-miofibroblastico-inflamatorio\" >Histologie de la tumeur myofibroblastique inflammatoire<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/patologia-tumoral-miofibroblastica-inflamatoria\/#Patologia-tumoral-miofibroblastica-inflamatoria\" >Pathologie tumorale myofibroblastique inflammatoire<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/patologia-tumoral-miofibroblastica-inflamatoria\/#Tinciones-especiales-para-tumor-miofibroblastico-inflamatorio\" >Taches sp\u00e9ciales pour tumeur myofibroblastique inflammatoire<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/patologia-tumoral-miofibroblastica-inflamatoria\/#Diagnostico-diferencial-del-tumor-miofibroblastico-inflamatorio-patologia\" >Diagnostic diff\u00e9rentiel de la pathologie tumorale myofibroblastique inflammatoire<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Introduccion\"><\/span>introduction<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span class=\"term\" data-term-id=\"490\">Inflammatoire<\/span> myofibroblastique <span class=\"term\" data-term-id=\"289\">tumeur<\/span> (IMT) appara\u00eet rarement sur la peau comme une croissance lente <span class=\"term\" data-term-id=\"52\">dermique<\/span> tumeur. De nombreuses tumeurs montrent <span class=\"term\" data-term-id=\"1849\">translocation<\/span> du <em>ALK <\/em><span class=\"term\" data-term-id=\"774\">g\u00e8ne<\/span>. Certaines de ces tumeurs ont \u00e9t\u00e9 \u00e9tiquet\u00e9es \u00abpseudotumeurs\u00bb ou \u00ab<span class=\"term\" data-term-id=\"1513\">plasma<\/span> cellule <span class=\"term\" data-term-id=\"113\">granulome<\/span>&#039; autrefois.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Histologia-del-tumor-miofibroblastico-inflamatorio\"><\/span>\n<span class=\"term\" data-term-id=\"128\">Histologie<\/span> de tumeur myofibroblastique inflammatoire<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span class=\"term\" data-term-id=\"1669\">Histologiquement<\/span>, la <span class=\"term\" data-term-id=\"164\">blessure<\/span> est bas\u00e9 sur le <span class=\"term\" data-term-id=\"61\">derme<\/span> et vu sous-jacent \u00e0 une normale <span class=\"term\" data-term-id=\"85\">\u00e9piderme<\/span> (Figure 1). La tumeur est compos\u00e9e d&#039;un m\u00e9lange de cellules ovo\u00efdes et fusiformes avec un inflammatoire pro\u00e9minent <span class=\"term\" data-term-id=\"541\">infiltrer<\/span> (Figures 2\u20133). L&#039;infiltrat est typiquement riche en plasmocytes (mieux visible sur la figure 2). Il peut y en avoir <span class=\"term\" data-term-id=\"1539\">pl\u00e9omorphisme<\/span> des cellules tumorales et certains <span class=\"term\" data-term-id=\"1536\">mitotique<\/span> figures (figure 3, fl\u00e8che).<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Patologia-tumoral-miofibroblastica-inflamatoria\"><\/span>Pathologie tumorale myofibroblastique inflammatoire<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='figure-1-2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-2615306-8950410' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/figure-1-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-2615306.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='figure-3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-3523557-4810226' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/Figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-3523557.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='figure-4__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-8951626-2751359' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/Figure-4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-8951626.jpg'>\n<\/div>\n<p class=\"p-small\">figure 3<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Tinciones-especiales-para-tumor-miofibroblastico-inflamatorio\"><\/span>Taches sp\u00e9ciales pour tumeur myofibroblastique inflammatoire<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Les cellules tumorales se colorent fortement avec la vimentine et de mani\u00e8re variable avec des marqueurs des muscles lisses. La SMA est positive dans jusqu&#039;\u00e0 901 cas de TP1T. ALK (<span class=\"term\" data-term-id=\"1327\">anaplasique<\/span> <span class=\"term\" data-term-id=\"976\">lymphome<\/span> kinase) <span class=\"term\" data-term-id=\"1421\">immunohistochimie<\/span> il est vu dans la plupart des cas et lorsqu&#039;il est vu, il est pratiquement diagnostique dans le bon contexte. <span class=\"term\" data-term-id=\"1237\">POISSON<\/span> Des tests de r\u00e9arrangements du g\u00e8ne ALK peuvent \u00e9galement \u00eatre utilis\u00e9s.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Diagnostico-diferencial-del-tumor-miofibroblastico-inflamatorio-patologia\"><\/span>\n<span class=\"term\" data-term-id=\"813\">Diagnostic diff\u00e9rentiel<\/span> de tumeur myofibroblastique inflammatoire <span class=\"term\" data-term-id=\"223\">pathologie<\/span><br \/>\n<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Diverses tumeurs m\u00e9senchymateuses inflammatoires: <span class=\"term\" data-term-id=\"1540\">Pl\u00e9omorphe<\/span> <span class=\"term\" data-term-id=\"1666\">sarcomes<\/span>, <span class=\"term\" data-term-id=\"1670\">m\u00e9lanome<\/span>et <span class=\"term\" data-term-id=\"1673\">l\u00e9iomyosarcome<\/span> ont des variantes inflammatoires.La positivit\u00e9 ALK par immunohistochimie FISH peut \u00eatre utile dans les cas difficiles.<\/p>\n<p>Pseudotumeur et granulome \u00e0 cellules plasmatiques: sans importance <span class=\"term\" data-term-id=\"1305\">atypie<\/span> et <em>ALK <\/em>g\u00e8ne <span class=\"term\" data-term-id=\"1850\">translocations<\/span>. De nombreux IMT ont \u00e9t\u00e9 qualifi\u00e9s de pseudotumeurs dans le pass\u00e9.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Introducci\u00f3n Inflamatorio miofibrobl\u00e1stico tumor (IMT) rara vez se presenta en la piel como un crecimiento lento d\u00e9rmico tumor. Muchos tumores muestran translocaci\u00f3n del ALK gene. Algunos de estos tumores fueron&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[205],"class_list":["post-16498","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones","tag-patologia"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/16498","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/comments?post=16498"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/16498\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/media?parent=16498"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/categories?post=16498"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/tags?post=16498"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}