{"id":6667,"date":"2020-04-22T16:11:50","date_gmt":"2020-04-22T19:11:50","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/paniculitis-histiocitica-citofagica\/"},"modified":"2020-04-27T17:10:03","modified_gmt":"2020-04-27T20:10:03","slug":"panniculite-histiocytaire-cytophagienne","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/","title":{"rendered":"Panniculite histiocytaire cytophagienne"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_87_1 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contenu<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Basculer la table des mati\u00e8res\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Basculer<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/#Que-es-paniculitis\" >Qu&#039;est-ce que la panniculite?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFQue-es-citofagico-histiocitico-paniculitis\" >Qu&#039;est-ce que le cytophage? panniculite histiocytaire?<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/#Paniculitis-histiocitica-citofagica\" >Panniculite histiocytaire cytophagienne<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-paniculitis-histiocitica-citofagica\" >Quelles sont les caract\u00e9ristiques cliniques de la panniculite histiocytaire cytophagienne?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFCual-es-la-causa-de-la-paniculitis-histiocitica-citofagica\" >Quelle est la cause de la panniculite histiocytaire cytophagienne?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFComo-se-diagnostica-la-paniculitis-histiocitica-citofagica\" >Comment diagnostique-t-on une panniculite histiocytaire cytophagienne?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/paniculitis-histiocitica-citofagica\/#%C2%BFCual-es-el-tratamiento-de-la-paniculitis-histiocitica-citofagica\" >Quel est le traitement de la panniculite histiocytaire cytophagienne?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Que-es-paniculitis\"><\/span>Qu&#039;est que c&#039;est <span class=\"term\" data-term-id=\"213\">panniculite<\/span>?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Panniculite<span> est un terme qui se r\u00e9f\u00e8re g\u00e9n\u00e9ralement \u00e0 un trouble de la <span class=\"term\" data-term-id=\"900\">sous-cutan\u00e9e<\/span> graisse.<\/span><\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-es-citofagico-histiocitico-paniculitis\"><\/span>Qu&#039;est-ce que le cytophage? <span class=\"term\" data-term-id=\"859\">histiocytaire<\/span> panniculite?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La panniculite histiocytaire cytophagienne est un <span class=\"term\" data-term-id=\"490\">inflammatoire<\/span> \u00e9tat graisseux sous-cutan\u00e9. Il est diagnostiqu\u00e9 apr\u00e8s <span class=\"term\" data-term-id=\"24\">biopsie<\/span> a d\u00e9tect\u00e9 anormal <span class=\"term\" data-term-id=\"858\">histiocytes<\/span> qui entourent d&#039;autres cellules (comme les globules rouges et blancs).<\/p>\n<p>La panniculite histiocytaire cytophagienne affecte \u00e9galement d&#039;autres organes et constitue une maladie mortelle.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Paniculitis-histiocitica-citofagica\"><\/span>Panniculite histiocytaire cytophagienne<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='panniculite cytophagique1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisinkildg1xq-3541678-6390383' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/cytophagic-panniculitis1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDg1XQ-3541678.jpg'>\n<\/div>\n<p class=\"p-small\">Panniculite histiocytaire cytophagienne<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='panniculite cytophagique2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-5382260-4292604' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/cytophagic-panniculitis2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-5382260.jpg'>\n<\/div>\n<p class=\"p-small\">Panniculite histiocytaire cytophagienne<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='panniculite cytophagique3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-6540464-5242445' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/cytophagic-panniculitis3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-6540464.jpg'>\n<\/div>\n<p class=\"p-small\">Panniculite histiocytaire cytophagienne<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-paniculitis-histiocitica-citofagica\"><\/span>Quelles sont les caract\u00e9ristiques cliniques de la panniculite histiocytaire cytophagienne?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La panniculite histiocytaire cytophagienne pr\u00e9sente une douleur sous-cutan\u00e9e <span class=\"term\" data-term-id=\"367\">nodules<\/span> sur plusieurs sites et <span class=\"term\" data-term-id=\"380\">syst\u00e9mique<\/span> sympt\u00f4mes<\/p>\n<ul>\n<li>Le patient se sent mal et a une <span class=\"term\" data-term-id=\"1176\">fi\u00e8vre<\/span>.<\/li>\n<li>Il y a une diminution des cellules et <span class=\"term\" data-term-id=\"616\">plaquettes<\/span> Dans le sang.<\/li>\n<li>Le foie et la rate sont hypertrophi\u00e9s.<\/li>\n<li>\n<span class=\"term\" data-term-id=\"1759\">Progressive<\/span> Une insuffisance h\u00e9patique se d\u00e9veloppe.<\/li>\n<\/ul>\n<p>La mort, lorsqu&#039;elle survient, est associ\u00e9e \u00e0 des saignements des voies gastro-intestinales, urinaires et respiratoires et dans la peau.  <\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-la-causa-de-la-paniculitis-histiocitica-citofagica\"><\/span>Quelle est la cause de la panniculite histiocytaire cytophagienne?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La panniculite histiocytaire cytophagienne est d\u00e9clench\u00e9e par une <span class=\"term\" data-term-id=\"145\">infection<\/span> dans environ 50% de cas<span style=\"font-size: 1rem;\">. Il s&#039;agit g\u00e9n\u00e9ralement d&#039;un des virus de l&#039;herp\u00e8s. La maladie survient chez les patients dont la fonction immunitaire est alt\u00e9r\u00e9e <\/span>immunod\u00e9ficience<span style=\"font-size: 1rem;\">, une <span class=\"term\" data-term-id=\"691\">auto-immune<\/span> maladie ou <span class=\"term\" data-term-id=\"1522\">h\u00e9matologique<\/span> maladie.<\/span><\/p>\n<p>Sous-cutan\u00e9e <span class=\"term\" data-term-id=\"631\">Cellule T<\/span> <span class=\"term\" data-term-id=\"976\">lymphome<\/span> Elle peut \u00e9galement pr\u00e9senter une panniculite histiocytaire cytophagienne.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-diagnostica-la-paniculitis-histiocitica-citofagica\"><\/span>Comment diagnostique-t-on une panniculite histiocytaire cytophagienne?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Biopsie d&#039;un sous-cutan\u00e9. <span class=\"term\" data-term-id=\"198\">nodule<\/span> montre des histiocytes cytophagiens et des cellules inflammatoires associ\u00e9s \u00e0 la d\u00e9composition et <span class=\"term\" data-term-id=\"120\">h\u00e9morragie<\/span> dans la graisse sous-cutan\u00e9e anormale <span class=\"term\" data-term-id=\"421\">lymphocytes<\/span> peut conduire \u00e0 un diagnostic de lymphome \u00e0 cellules T. <\/p>\n<p>Des recherches suppl\u00e9mentaires peuvent montrer des dommages \u00e0 d&#039;autres organes et une tendance au saignement. Il peut y avoir des signes d&#039;une infection ant\u00e9rieure, comme un virus de l&#039;herp\u00e8s, et d&#039;une alt\u00e9ration de la fonction immunitaire. Si un lymphome \u00e0 cellules T est diagnostiqu\u00e9, la stadification peut trouver des signes de lymphome <span class=\"term\" data-term-id=\"1775\">ganglions lymphatiques<\/span> et ailleurs<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-el-tratamiento-de-la-paniculitis-histiocitica-citofagica\"><\/span>Quel est le traitement de la panniculite histiocytaire cytophagienne?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La panniculite histiocytaire cytophagienne est souvent mortelle si elle n&#039;est pas trait\u00e9e.  <\/p>\n<p>Le traitement symptomatique consiste en une transfusion et une corticoth\u00e9rapie. L&#039;\u00e9toposide et la cyclosporine se sont r\u00e9v\u00e9l\u00e9s utiles dans certains cas. Certains auteurs recommandent que la panniculite histiocytaire cytophagienne soit trait\u00e9e par chimioth\u00e9rapie de type CHOP. De bons r\u00e9sultats ont \u00e9t\u00e9 obtenus avec des doses intraveineuses \u00e9lev\u00e9es. <span class=\"term\" data-term-id=\"427\">immunoglobuline<\/span>.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Que es paniculitis? Paniculitis es un t\u00e9rmino que generalmente se refiere a un trastorno de la subcut\u00e1neo grasa. \u00bfQu\u00e9 es citof\u00e1gico? histioc\u00edtico paniculitis? La paniculitis histioc\u00edtica citof\u00e1gica es un inflamatorio&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-6667","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/6667","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/comments?post=6667"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/6667\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/media?parent=6667"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/categories?post=6667"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/tags?post=6667"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}