{"id":6809,"date":"2020-04-23T06:43:08","date_gmt":"2020-04-23T09:43:08","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/enfermedad-de-dercum\/"},"modified":"2020-04-27T16:52:02","modified_gmt":"2020-04-27T19:52:02","slug":"maladie-du-dercum","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/fr\/wiki\/enfermedad-de-dercum\/","title":{"rendered":"Maladie de Dercum"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contenu<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Basculer la table des mati\u00e8res\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Basculer<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/enfermedad-de-dercum\/#%C2%BFQue-es-la-enfermedad-de-Dercum\" >Qu\u2019est-ce que la maladie de Dercum ?<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/enfermedad-de-dercum\/#Lipomas-dolorosos-multiples\" >Multiples lipomes douloureux<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/enfermedad-de-dercum\/#%C2%BFQuien-contrae-la-enfermedad-de-Dercum\" >Qui contracte la maladie de Dercum ?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/enfermedad-de-dercum\/#%C2%BFComo-se-diagnostica-la-enfermedad-de-Dercum\" >Comment diagnostique-t-on la maladie de Dercum ?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/enfermedad-de-dercum\/#%C2%BFCual-es-el-tratamiento-para-la-enfermedad-de-Dercum\" >Quel est le traitement de la maladie de Dercum ?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-es-la-enfermedad-de-Dercum\"><\/span>Qu\u2019est-ce que la maladie de Dercum ?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>La maladie du derme est \u00e9galement connue sous le nom d\u2019adipose douloureuse. Il s\u2019agit d\u2019une maladie rare caract\u00e9ris\u00e9e par une combinaison de caract\u00e9ristiques :<\/p>\n<ul>\n<li>Plusieurs <span class=\"term\" data-term-id=\"1705\">encapsul\u00e9<\/span> croissance excessive de graisse (lipomes) sur le tronc et les extr\u00e9mit\u00e9s<\/li>\n<li>Douloureux <span class=\"term\" data-term-id=\"900\">sous-cutan\u00e9e<\/span> <span class=\"term\" data-term-id=\"368\">assiettes<\/span>\n<\/li>\n<li>\n<span class=\"term\" data-term-id=\"76\">Ecchymose<\/span> (ecchymoses) sans s&#039;en apercevoir <span class=\"term\" data-term-id=\"1365\">traumatisme<\/span>\n<\/li>\n<\/ul>\n<p>Les maladies cutan\u00e9es peuvent \u00eatre associ\u00e9es \u00e0 l\u2019ob\u00e9sit\u00e9, \u00e0 la d\u00e9tresse \u00e9motionnelle et \u00e0 la fatigue.<\/p>\n<p>Elle a \u00e9t\u00e9 d\u00e9crite pour la premi\u00e8re fois en 1892 par Dercum, qui appelait la maladie \u00ab adipose douloureuse \u00bb pour d\u00e9crire les adiposit\u00e9s douloureuses (accumulations de graisse) observ\u00e9es chez ses 3 patients.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Lipomas-dolorosos-multiples\"><\/span>Multiples lipomes douloureux<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='dercum-1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-2679675-4677358' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/dercum-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-2679675.jpg'>\n<\/div>\n<p class=\"p-small\">lipomes douloureux<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='dercum-2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-5470233-4723999' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/dercum-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-5470233.jpg'>\n<\/div>\n<p class=\"p-small\">lipomes douloureux<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQuien-contrae-la-enfermedad-de-Dercum\"><\/span>Qui contracte la maladie de Dercum ?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<ul>\n<li>La maladie des \u00e9panchements touche plus souvent les femmes que les hommes (elle serait 5 \u00e0 30 fois plus fr\u00e9quente chez les femmes que chez les hommes).<\/li>\n<li>Elle appara\u00eet g\u00e9n\u00e9ralement entre 35 et 50 ans.<\/li>\n<li>Cela peut \u00eatre plus fr\u00e9quent chez les personnes ob\u00e8ses.<\/li>\n<\/ul>\n<p>La plupart des personnes atteintes de la maladie de Dercum n\u2019ont pas d\u2019ant\u00e9c\u00e9dents familiaux de maladie de Dercum. Cependant, il a \u00e9t\u00e9 rapport\u00e9 que la maladie pr\u00e9sente une <span class=\"term\" data-term-id=\"828\">autosomique<\/span> mod\u00e8le de transmission dominant dans certaines familles (c&#039;est-\u00e0-dire que les enfants d&#039;une personne atteinte de la maladie de Dercum ont \u00e9galement 1 chance sur 2 de la d\u00e9velopper).<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-diagnostica-la-enfermedad-de-Dercum\"><\/span>Comment diagnostique-t-on la maladie de Dercum ?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Un diagnostic de maladie de Dercum peut \u00eatre pos\u00e9 par un examen physique syst\u00e9matique et l&#039;identification de la triade caract\u00e9ristique (lipomes multiples, plaques douloureuses et ob\u00e9sit\u00e9).<\/p>\n<p>De multiples lipomes peuvent \u00e9galement \u00eatre caract\u00e9ristiques de\u00a0:<\/p>\n<ul>\n<li>Lipomatose multiple (<span class=\"term\" data-term-id=\"849\">famille<\/span> ou sporadique)<\/li>\n<li>Fibromyalgie<\/li>\n<li><span class=\"term\" data-term-id=\"213\">Panniculite<\/span><\/li>\n<li>Ob\u00e9sit\u00e9 sans plaques douloureuses.<\/li>\n<li>\n<p>Cushing <span class=\"term\" data-term-id=\"350\">syndrome<\/span>, ce qui peut \u00e9galement conduire \u00e0 une graisse anormale <span class=\"term\" data-term-id=\"69\">Distribution<\/span> et des ecchymoses<\/li>\n<\/ul>\n<p>ONGLE <span class=\"term\" data-term-id=\"24\">biopsie<\/span> peut \u00eatre utile pour distinguer un lipome d&#039;un <span class=\"term\" data-term-id=\"364\">angiolipome<\/span> (un autre type de prolif\u00e9ration douloureuse de graisse).<\/p>\n<p>D&#039;autres l\u00e9sions pouvant ressembler \u00e0 des lipomes comprennent<\/p>\n<ul>\n<li>Kystes \u00e9pidermo\u00efdes (qui ont g\u00e9n\u00e9ralement un point lacrymal central)<\/li>\n<li>Hibernome (un <span class=\"term\" data-term-id=\"22\">b\u00e9nin<\/span> croissance de graisse brune)<\/li>\n<li>Hernie lipofasciale (une hernie dans l&#039;anus ou <span class=\"term\" data-term-id=\"1192\">p\u00e9rianale<\/span> r\u00e9gion)<\/li>\n<li>Lipoedema<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-el-tratamiento-para-la-enfermedad-de-Dercum\"><\/span>Quel est le traitement de la maladie de Dercum ?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Les maladies intestinales semblent b\u00e9n\u00e9ficier de la perte de poids du patient. Chirurgical <span class=\"term\" data-term-id=\"848\">excision<\/span> ou une liposuccion de lipomes s\u00e9lectionn\u00e9s peut aider, surtout lorsqu&#039;ils se trouvent dans des endroits peu pratiques. L&#039;excision chirurgicale de nombreux lipomes n&#039;est g\u00e9n\u00e9ralement pas consid\u00e9r\u00e9e comme utile et risque de complications chirurgicales.<\/p>\n<p>Les analg\u00e9siques conventionnels ne semblent pas r\u00e9duire l&#039;inconfort associ\u00e9 \u00e0 la maladie de Dercum. Certains rapports sugg\u00e8rent qu&#039;un local <span class=\"term\" data-term-id=\"1206\">anesth\u00e9sique<\/span> injection ou <span class=\"term\" data-term-id=\"224\">pi\u00e8ce<\/span> Cela peut soulager une douleur insurmontable.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>\u00bfQu\u00e9 es la enfermedad de Dercum? La enfermedad del dermis tambi\u00e9n se conoce como adiposis dolorosa. Es una enfermedad rara caracterizada por una combinaci\u00f3n de caracter\u00edsticas: M\u00faltiple encapsulado crecimiento excesivo&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-6809","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/6809","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/comments?post=6809"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/6809\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/media?parent=6809"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/categories?post=6809"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/tags?post=6809"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}