{"id":6953,"date":"2020-04-23T21:28:38","date_gmt":"2020-04-24T00:28:38","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/angiofibroma-patologia-2\/"},"modified":"2020-05-03T18:25:08","modified_gmt":"2020-05-03T21:25:08","slug":"angiofibrome-pathologie-2","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/fr\/wiki\/angiofibroma-patologia-2\/","title":{"rendered":"Pathologie de l&#039;angiofibrome"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_89 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Contenu<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Basculer la table des mati\u00e8res\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Basculer<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/angiofibroma-patologia-2\/#Introduccion\" >introduction<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/angiofibroma-patologia-2\/#Histologia-de-angiofibroma\" >Histologie de l&#039;angiofibrome<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/angiofibroma-patologia-2\/#Angiofibroma-patologia\" >Pathologie de l&#039;angiofibrome<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/angiofibroma-patologia-2\/#Estudios-especiales-para-angiofibroma\" >\u00c9tudes sp\u00e9ciales pour l&#039;angiofibrome.<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/fr\/wiki\/angiofibroma-patologia-2\/#Diagnostico-diferencial-de-angiofibroma-patologia\" >Diagnostic diff\u00e9rentiel de la pathologie de l&#039;angiofibrome<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Introduccion\"><\/span>introduction<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Il existe de nombreuses formes cliniques diff\u00e9rentes de <span class=\"term\" data-term-id=\"336\">angiofibromes<\/span> ils partagent un identique <span class=\"term\" data-term-id=\"129\">histopathologie<\/span>:<\/p>\n<ul>\n<li>Fibreux <span class=\"term\" data-term-id=\"217\">papule<\/span><\/li>\n<li>P\u00e9nis perl\u00e9 <span class=\"term\" data-term-id=\"366\">papules<\/span><\/li>\n<li>\n<span class=\"term\" data-term-id=\"597\">ad\u00e9nome<\/span> s\u00e9bac\u00e9es (angiofibomes faciaux associ\u00e9s aux tub\u00e9reuses <span class=\"term\" data-term-id=\"260\">scl\u00e9rose<\/span>)<\/li>\n<li>Syndromique <span class=\"term\" data-term-id=\"335\">angiofibrome<\/span>\n<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"Histologia-de-angiofibroma\"><\/span>\n<span class=\"term\" data-term-id=\"128\">Histologie<\/span> angiofibrome<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Les angiofibromes provoquent une masse en forme de d\u00f4me \u00e0 la surface <span class=\"term\" data-term-id=\"61\">derme<\/span> (Figure 1). Le sous-jacent <span class=\"term\" data-term-id=\"85\">\u00e9piderme<\/span> pas impliqu\u00e9 mais il peut \u00eatre <span class=\"term\" data-term-id=\"809\">atrophique<\/span>. Les <span class=\"term\" data-term-id=\"164\">blessure<\/span> se caract\u00e9rise par un <span class=\"term\" data-term-id=\"893\">prolif\u00e9ration<\/span> de cellules \u00e9toil\u00e9es et en spirale autour <span class=\"term\" data-term-id=\"953\">vaisseaux sanguins<\/span> (Figure 2). Il y a une \u00e9paisseur concentrique <span class=\"term\" data-term-id=\"39\">collag\u00e8ne<\/span> colis (figures 1, 2). La comparaison de la densit\u00e9 de collag\u00e8ne de la l\u00e9sion avec le derme environnant, qui devrait \u00eatre plus l\u00e2che ou endommag\u00e9 \u00e9lastiquement, peut \u00eatre un indice de diagnostic utile. Parfois un peu <span class=\"term\" data-term-id=\"490\">inflammatoire<\/span> cellule <span class=\"term\" data-term-id=\"541\">infiltrer<\/span> de <span class=\"term\" data-term-id=\"421\">lymphocytes<\/span> il est pr\u00e9sent.<\/p>\n<p>Divers <span class=\"term\" data-term-id=\"474\">histologique<\/span> Des sous-types ont \u00e9t\u00e9 d\u00e9crits:<\/p>\n<ul>\n<li>L&#039;angiofibrome hypercellulaire se caract\u00e9rise par un plus grand nombre de cellules \u00e9toil\u00e9es et fusiformes (figure 3).<\/li>\n<li>L&#039;angofibrome \u00e0 cellules claires montre une prolif\u00e9ration de cellules granuleuses \u00e0 mousseuses qui ressemble \u00e0 <span class=\"term\" data-term-id=\"858\">histiocytes<\/span>.<\/li>\n<li>\n<span class=\"term\" data-term-id=\"1540\">Pl\u00e9omorphe<\/span> l&#039;angiofibrome est caract\u00e9ris\u00e9 par d&#039;\u00e9tranges \u00e9toiles <span class=\"term\" data-term-id=\"101\">fibroblastes<\/span>.<\/li>\n<li>UNE <span class=\"term\" data-term-id=\"1667\">\u00e9pith\u00e9lio\u00efde<\/span> La variante de l&#039;angiofibrome se compose de cellules de type \u00e9pith\u00e9lio\u00efde avec rose <span class=\"term\" data-term-id=\"838\">cytoplasme<\/span> et nucl\u00e9oles pro\u00e9minents.<\/li>\n<\/ul>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Angiofibroma-patologia\"><\/span>Pathologie de l&#039;angiofibrome<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='angiofibrome-figure-1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-6854273-7505044' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/angiofibroma-figure-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-6854273.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='angiofibroma-figure-2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-5148991-5214304' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/angiofibroma-figure-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-5148991.jpg'>\n<\/div>\n<p class=\"p-small\">Figure 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='angiofibrome-figure-3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-7103142-2420591' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/angiofibroma-figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-7103142.jpg'>\n<\/div>\n<p class=\"p-small\">figure 3<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Estudios-especiales-para-angiofibroma\"><\/span>\u00c9tudes sp\u00e9ciales pour l&#039;angiofibrome.<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span class=\"term\" data-term-id=\"52\">Dermique<\/span> <span class=\"term\" data-term-id=\"51\">cellules dendritiques<\/span> il est g\u00e9n\u00e9ralement color\u00e9 pour le facteur XIIIa. S100 est n\u00e9gatif.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Diagnostico-diferencial-de-angiofibroma-patologia\"><\/span>\n<span class=\"term\" data-term-id=\"813\">Diagnostic diff\u00e9rentiel<\/span> angiofibrome <span class=\"term\" data-term-id=\"223\">pathologie<\/span><br \/>\n<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Scl\u00e9rosant <span class=\"term\" data-term-id=\"353\">naevus<\/span> - Ceux-ci ne pr\u00e9sentent g\u00e9n\u00e9ralement pas <span class=\"term\" data-term-id=\"753\">vasculaire<\/span> ectasie La tache S100 mettra en \u00e9vidence la <span class=\"term\" data-term-id=\"181\">m\u00e9lanocytes<\/span>, et sera n\u00e9gatif dans les papules fibreuses.<\/p>\n<p><span class=\"term\" data-term-id=\"756\">Capillaire<\/span> <span class=\"term\" data-term-id=\"360\">h\u00e9mangiome<\/span> - Ceux-ci manquent de fibres <span class=\"term\" data-term-id=\"1655\">stroma<\/span> avec des fibroblastes \u00e9toil\u00e9s et du collag\u00e8ne dense.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Introducci\u00f3n Existen numerosas formas cl\u00ednicas distintas de angiofibromas que comparten un id\u00e9ntico histopatolog\u00eda: Fibroso p\u00e1pula Pene perlado p\u00e1pulas adenoma sebaceo (angiofibomas faciales asociados con tuberosas esclerosis) Sindr\u00f3mico angiofibroma Histolog\u00eda de&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[205],"class_list":["post-6953","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones","tag-patologia"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/6953","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/comments?post=6953"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/wiki\/6953\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/media?parent=6953"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/categories?post=6953"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/fr\/wp-json\/wp\/v2\/tags?post=6953"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}