{"id":16716,"date":"2020-04-29T08:15:05","date_gmt":"2020-04-29T11:15:05","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/"},"modified":"2020-05-03T10:29:59","modified_gmt":"2020-05-03T13:29:59","slug":"doenca-de-pele-paget-mamaria","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/","title":{"rendered":"Doen\u00e7a de Paget na pele"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Conte\u00fado<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabela de conte\u00fado\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Alternar<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/#%C2%BFQue-es-la-enfermedad-de-Paget-mamaria\" >O que \u00e9 a doen\u00e7a mam\u00e1ria de Paget?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/#%C2%BFQuien-contrae-la-enfermedad-de-Paget-mamaria\" >Quem contrai a doen\u00e7a de Paget na mama?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/#%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-enfermedad-de-Paget-mamaria\" >Quais s\u00e3o as caracter\u00edsticas cl\u00ednicas da doen\u00e7a de Paget mam\u00e1ria?<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/#Enfermedad-de-Paget-mamaria\" >Doen\u00e7a de Paget da mama<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/#%C2%BFComo-se-diagnostica-la-enfermedad-de-Paget-mamaria\" >Como \u00e9 diagnosticada a doen\u00e7a mam\u00e1ria de Paget?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/#Cual-es-el-diagnostico-diferencial-para-la-enfermedad-de-Paget-mamaria\" >Qual \u00e9 o diagn\u00f3stico diferencial da doen\u00e7a de Paget mam\u00e1ria?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/enfermedad-mamaria-de-paget-de-la-piel\/#%C2%BFCual-es-el-tratamiento-de-la-enfermedad-de-Paget-mamaria\" >Qual \u00e9 o tratamento da doen\u00e7a de Paget da mama?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-es-la-enfermedad-de-Paget-mamaria\"><\/span>O que \u00e9 a doen\u00e7a mam\u00e1ria de Paget?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>A doen\u00e7a cut\u00e2nea de Paget mam\u00e1ria \u00e9 uma doen\u00e7a cut\u00e2nea rara <span class=\"term\" data-term-id=\"30\">C\u00e2ncer<\/span> caracterizado por um <span class=\"term\" data-term-id=\"319\">cr\u00f4nica<\/span> <span class=\"term\" data-term-id=\"491\">eczema<\/span>-eu gosto <span class=\"term\" data-term-id=\"255\">erup\u00e7\u00e3o<\/span> do mamilo e <span class=\"term\" data-term-id=\"1351\">adjacente<\/span> <span class=\"term\" data-term-id=\"1492\">areolar<\/span> pelagem. Tamb\u00e9m chamada de doen\u00e7a do mamilo de Paget.<\/p>\n<p>A doen\u00e7a de Paget da mama est\u00e1 associada ao c\u00e2ncer subjacente, seja <span class=\"term\" data-term-id=\"1077\">no lugar<\/span> adenocarcinoma da mama ou mais <span class=\"term\" data-term-id=\"309\">estendido<\/span> c\u00e2ncer infiltrativo, embora \u00e0s vezes seja dif\u00edcil de detectar no exame cl\u00ednico ou na mamografia.<\/p>\n<p>Uma condi\u00e7\u00e3o semelhante que afeta a pele da genit\u00e1lia feminina e masculina \u00e9 conhecida como doen\u00e7a de Paget extramam\u00e1ria.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQuien-contrae-la-enfermedad-de-Paget-mamaria\"><\/span>Quem contrai a doen\u00e7a de Paget na mama?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>A doen\u00e7a mam\u00e1ria de Paget \u00e9 mais frequentemente diagnosticada entre as idades de 50 e 60 anos. \u00c9 muito mais comum em mulheres do que em homens. <\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-enfermedad-de-Paget-mamaria\"><\/span>Quais s\u00e3o as caracter\u00edsticas cl\u00ednicas da doen\u00e7a de Paget mam\u00e1ria?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>A maioria dos pacientes com doen\u00e7a de Paget na mama queixa-se de erup\u00e7\u00e3o cut\u00e2nea com coceira e queima\u00e7\u00e3o na \u00e1rea do mamilo e ao redor dela. \u00c0s vezes, a pele pode romper e doer devido \u00e0 coceira. Outros sintomas incluem:<\/p>\n<ul>\n<li>Vermelhid\u00e3o<\/li>\n<li>Incha\u00e7o<\/li>\n<li>mamilo escorrendo <span class=\"term\" data-term-id=\"840\">baixar<\/span>\n<\/li>\n<li><span class=\"term\" data-term-id=\"384\">Escalada<\/span><\/li>\n<li>Corrimento sangrento do mamilo<\/li>\n<li><span class=\"term\" data-term-id=\"1278\">Ulcera\u00e7\u00e3o<\/span><\/li>\n<li>Invers\u00e3o do mamilo.<\/li>\n<\/ul>\n<p><span class=\"term\" data-term-id=\"385\">Escamoso<\/span>crocante e espesso <span class=\"term\" data-term-id=\"368\">pratos<\/span> Freq\u00fcentemente, eles se formam no mamilo, que ent\u00e3o se espalha para a \u00e1rea circundante. Normalmente, apenas um mamilo \u00e9 afetado, embora tenham sido observados casos raros de ambos os mamilos afetados.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Enfermedad-de-Paget-mamaria\"><\/span>Doen\u00e7a de Paget da mama<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='paget1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisinkildrd-9349773-2753076' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/paget1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDRd-9349773.jpg'>\n<\/div>\n<p class=\"p-small\">F\u00eamea<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='paget3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildbd-2580855-6105295' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/paget3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDBd-2580855.jpg'>\n<\/div>\n<p class=\"p-small\">F\u00eamea<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='paget2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-7257058-1183399' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/paget2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-7257058.jpg'>\n<\/div>\n<p class=\"p-small\">Masculino<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-diagnostica-la-enfermedad-de-Paget-mamaria\"><\/span>Como \u00e9 diagnosticada a doen\u00e7a mam\u00e1ria de Paget?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Embora possa ser suspeitado clinicamente, uma les\u00e3o cut\u00e2nea <span class=\"term\" data-term-id=\"24\">bi\u00f3psia<\/span> do <span class=\"term\" data-term-id=\"164\">ferimentos<\/span> \u00c9 realizado para um diagn\u00f3stico preciso da doen\u00e7a de Paget da mama. Sob o microsc\u00f3pio, a presen\u00e7a de c\u00e9lulas de Paget juntamente com outras <span class=\"term\" data-term-id=\"474\">histol\u00f3gico<\/span> Os achados confirmam o diagn\u00f3stico. Uma bi\u00f3psia de pele tamb\u00e9m pode determinar se h\u00e1 c\u00e2ncer subjacente, embora alguns carcinomas de mama n\u00e3o sejam detectados porque est\u00e3o localizados mais profundamente no tecido mam\u00e1rio. Uma mamografia pode ser realizada para identificar o c\u00e2ncer subjacente antes de uma bi\u00f3psia de mama.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Cual-es-el-diagnostico-diferencial-para-la-enfermedad-de-Paget-mamaria\"><\/span>Qual \u00e9 ele <span class=\"term\" data-term-id=\"813\"><span class=\"term\" data-term-id=\"813\">diagn\u00f3stico diferencial<\/span><\/span> para doen\u00e7a de Paget mam\u00e1ria?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>a <span class=\"term tooltipstered\" data-term-id=\"813\">diagn\u00f3stico diferencial<\/span> para a doen\u00e7a de Paget da mama inclui:<\/p>\n<ul>\n<li>\n<p>Eczema mamilar (muito mais comum que a doen\u00e7a mam\u00e1ria de Paget, especialmente em adolescentes e adultos jovens)<\/li>\n<li>Mamilo <span class=\"term\" data-term-id=\"215\">papilomatose<\/span><\/li>\n<li><span class=\"term\" data-term-id=\"610\">Hiperqueratose<\/span> do mamilo e <span class=\"term\" data-term-id=\"1490\">ar\u00e9ola<\/span><\/li>\n<li><span class=\"term\" data-term-id=\"1038\">Intraepid\u00e9rmico<\/span> <span class=\"term\" data-term-id=\"270\">escamoso<\/span> c\u00e9lula <span class=\"term\" data-term-id=\"32\">carcinoma<\/span><\/li>\n<\/ul>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\"><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCual-es-el-tratamiento-de-la-enfermedad-de-Paget-mamaria\"><\/span>Qual \u00e9 o tratamento da doen\u00e7a de Paget da mama?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>A mastectomia (remo\u00e7\u00e3o da mama) costuma ser o tratamento necess\u00e1rio para a doen\u00e7a mam\u00e1ria de Paget. Alternativamente, pode ser removido localmente amplamente, juntamente com amostras de tecido colhidas de perto. <span class=\"term\" data-term-id=\"1775\">g\u00e2nglios linf\u00e1ticos<\/span> na axila \u00c0s vezes, tratamento conservador, como mamilo parcial. <span class=\"term\" data-term-id=\"848\">excis\u00e3o<\/span>, clivagem em cunha, clivagem em cone, <span class=\"term\" data-term-id=\"1325\">radioterapia<\/span>, ou uma combina\u00e7\u00e3o destes pode ser usada em mulheres com est\u00e1gios menos avan\u00e7ados da doen\u00e7a. Por\u00e9m, <span class=\"term\" data-term-id=\"1074\">reaparecimento<\/span> \u00c9 comum nesses casos.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>\u00bfQu\u00e9 es la enfermedad de Paget mamaria? La enfermedad de Paget mamaria de la piel es una piel poco com\u00fan c\u00e1ncer caracterizado por un cr\u00f3nico eczema-me gusta erupci\u00f3n del pez\u00f3n&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[],"class_list":["post-16716","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki\/16716","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/comments?post=16716"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki\/16716\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/media?parent=16716"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/categories?post=16716"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/tags?post=16716"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}