{"id":6953,"date":"2020-04-23T21:28:38","date_gmt":"2020-04-24T00:28:38","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/angiofibroma-patologia-2\/"},"modified":"2020-05-03T18:25:08","modified_gmt":"2020-05-03T21:25:08","slug":"angiofibroma-patologia-2","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/pt\/wiki\/angiofibroma-patologia-2\/","title":{"rendered":"Patologia de Angiofibroma"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Conte\u00fado<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabela de conte\u00fado\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Alternar<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/angiofibroma-patologia-2\/#Introduccion\" >Introdu\u00e7\u00e3o<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/angiofibroma-patologia-2\/#Histologia-de-angiofibroma\" >Angiofibroma Histologia<\/a><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><ul class='ez-toc-list-level-5' ><li class='ez-toc-heading-level-5'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/angiofibroma-patologia-2\/#Angiofibroma-patologia\" >Patologia de Angiofibroma<\/a><\/li><\/ul><\/li><\/ul><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/angiofibroma-patologia-2\/#Estudios-especiales-para-angiofibroma\" >Estudos especiais para angiofibroma.<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/angiofibroma-patologia-2\/#Diagnostico-diferencial-de-angiofibroma-patologia\" >Diagn\u00f3stico diferencial da patologia do angiofibroma<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"Introduccion\"><\/span>Introdu\u00e7\u00e3o<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Existem muitas formas cl\u00ednicas diferentes de <span class=\"term\" data-term-id=\"336\">angiofibromas<\/span> que compartilham um id\u00eantico <span class=\"term\" data-term-id=\"129\">histopatologia<\/span>:<\/p>\n<ul>\n<li>Fibroso <span class=\"term\" data-term-id=\"217\">p\u00e1pula<\/span><\/li>\n<li>p\u00eanis perolado <span class=\"term\" data-term-id=\"366\">p\u00e1pulas<\/span><\/li>\n<li>\n<span class=\"term\" data-term-id=\"597\">adenoma<\/span> seb\u00e1ceos (angiofibromas faciais associados a <span class=\"term\" data-term-id=\"260\">esclerose<\/span>)<\/li>\n<li>Sindr\u00f4mico <span class=\"term\" data-term-id=\"335\">angiofibroma<\/span>\n<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"Histologia-de-angiofibroma\"><\/span>\n<span class=\"term\" data-term-id=\"128\">Histologia<\/span> de angiofibroma<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Os angiofibromas causam uma massa em forma de c\u00fapula na superf\u00edcie <span class=\"term\" data-term-id=\"61\">derme<\/span> (Figura 1). o sobrejacente <span class=\"term\" data-term-id=\"85\">epiderme<\/span> n\u00e3o est\u00e1 envolvido, mas pode estar <span class=\"term\" data-term-id=\"809\">atr\u00f3fico<\/span>. a <span class=\"term\" data-term-id=\"164\">ferimentos<\/span> \u00e9 caracterizada por uma <span class=\"term\" data-term-id=\"893\">prolifera\u00e7\u00e3o<\/span> de c\u00e9lulas estreladas e espirais ao redor <span class=\"term\" data-term-id=\"953\">vasos sangu\u00edneos<\/span> (Figura 2). H\u00e1 espessura conc\u00eantrica <span class=\"term\" data-term-id=\"39\">col\u00e1geno<\/span> pacotes (figuras 1, 2). A compara\u00e7\u00e3o da densidade de col\u00e1geno da les\u00e3o com a derme circundante, que deve estar mais frouxa ou danificada elastoticamente, pode ser uma pista diagn\u00f3stica \u00fatil. Ocasionalmente um escasso <span class=\"term\" data-term-id=\"490\">inflamat\u00f3rio<\/span> c\u00e9lula <span class=\"term\" data-term-id=\"541\">infiltrar<\/span> do <span class=\"term\" data-term-id=\"421\">linf\u00f3citos<\/span> est\u00e1 presente.<\/p>\n<p>V\u00e1rios <span class=\"term\" data-term-id=\"474\">histol\u00f3gico<\/span> Os subtipos foram descritos:<\/p>\n<ul>\n<li>O angiofibroma hipercelular \u00e9 caracterizado por um maior n\u00famero de c\u00e9lulas estreladas e fusiformes (figura 3).<\/li>\n<li>O angofibroma de c\u00e9lulas claras mostra uma prolifera\u00e7\u00e3o de c\u00e9lulas granulares a espumosas, lembrando <span class=\"term\" data-term-id=\"858\">histi\u00f3citos<\/span>.<\/li>\n<li>\n<span class=\"term\" data-term-id=\"1540\">Pleom\u00f3rfico<\/span> angiofibroma \u00e9 caracterizado por estranhas, estreladas <span class=\"term\" data-term-id=\"101\">fibroblastos<\/span>.<\/li>\n<li>UMA <span class=\"term\" data-term-id=\"1667\">epiteli\u00f3ide<\/span> A variante do angiofibroma consiste em c\u00e9lulas semelhantes a epitelioides com <span class=\"term\" data-term-id=\"838\">citoplasma<\/span> e nucl\u00e9olos proeminentes.<\/li>\n<\/ul>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\"><span class=\"ez-toc-section\" id=\"Angiofibroma-patologia\"><\/span>Patologia de Angiofibroma<span class=\"ez-toc-section-end\"><\/span><\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='angiofibroma-figure-1__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-6854273-7505044' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/angiofibroma-figure-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-6854273.jpg'>\n<\/div>\n<p class=\"p-small\">figura 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='angiofibroma-figure-2__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-5148991-5214304' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/angiofibroma-figure-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-5148991.jpg'>\n<\/div>\n<p class=\"p-small\">Figura 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img alt='angiofibroma-figure-3__protectwyjqcm90zwn0il0_focusfillwzi5ncwymjisingildfd-7103142-2420591' src='https:\/\/doctorhoogstra.com\/wp-content\/uploads\/2020\/04\/angiofibroma-figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd-7103142.jpg'>\n<\/div>\n<p class=\"p-small\">Figura 3<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Estudios-especiales-para-angiofibroma\"><\/span>Estudos especiais para angiofibroma.<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p><span class=\"term\" data-term-id=\"52\">D\u00e9rmica<\/span> <span class=\"term\" data-term-id=\"51\">c\u00e9lulas dendr\u00edticas<\/span> geralmente cora para o fator XIIIa. S100 \u00e9 negativo.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Diagnostico-diferencial-de-angiofibroma-patologia\"><\/span>\n<span class=\"term\" data-term-id=\"813\">Diagn\u00f3stico diferencial<\/span> de angiofibroma <span class=\"term\" data-term-id=\"223\">patologia<\/span><br \/>\n<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>esclerosante <span class=\"term\" data-term-id=\"353\">nevo<\/span> \u2013 Geralmente n\u00e3o apresentam <span class=\"term\" data-term-id=\"753\">vascular<\/span> ectasia A colora\u00e7\u00e3o S100 destacar\u00e1 a <span class=\"term\" data-term-id=\"181\">melan\u00f3citos<\/span>, e ser\u00e1 negativo em p\u00e1pulas fibrosas.<\/p>\n<p><span class=\"term\" data-term-id=\"756\">Capilar<\/span> <span class=\"term\" data-term-id=\"360\">hemangioma<\/span> - Estes n\u00e3o t\u00eam o fibroso <span class=\"term\" data-term-id=\"1655\">estroma<\/span> com fibroblastos estrelados e col\u00e1geno denso.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>Introducci\u00f3n Existen numerosas formas cl\u00ednicas distintas de angiofibromas que comparten un id\u00e9ntico histopatolog\u00eda: Fibroso p\u00e1pula Pene perlado p\u00e1pulas adenoma sebaceo (angiofibomas faciales asociados con tuberosas esclerosis) Sindr\u00f3mico angiofibroma Histolog\u00eda de&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[204],"tags":[205],"class_list":["post-6953","wiki","type-wiki","status-publish","format-standard","category-glosario-definiciones","tag-patologia"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki\/6953","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/comments?post=6953"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki\/6953\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/media?parent=6953"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/categories?post=6953"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/tags?post=6953"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}