{"id":8244,"date":"2020-04-27T20:53:08","date_gmt":"2020-04-27T23:53:08","guid":{"rendered":"https:\/\/doctorhoogstra.com\/es\/wiki\/malformacion-glomuvenosa\/"},"modified":"2020-04-27T20:53:08","modified_gmt":"2020-04-27T23:53:08","slug":"malformacao-glomurosa","status":"publish","type":"wiki","link":"https:\/\/doctorhoogstra.com\/pt\/wiki\/malformacion-glomuvenosa\/","title":{"rendered":"Malforma\u00e7\u00e3o glomurosa"},"content":{"rendered":"<p><\/p><div id=\"ez-toc-container\" class=\"ez-toc-v2_0_88 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Conte\u00fado<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabela de conte\u00fado\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Alternar<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewbox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewbox=\"0 0 24 24\" version=\"1.2\" baseprofile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 eztoc-toggle-hide-by-default' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/malformacion-glomuvenosa\/#%C2%BFQue-es-un-glomuvenoso-malformacion\" >O que \u00e9 um glomuvenous? malforma\u00e7\u00e3o?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/malformacion-glomuvenosa\/#%C2%BFQuien-contrae-malformacion-glomuvenosa\" >Quem recebe uma malforma\u00e7\u00e3o glomuvenescedora?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/malformacion-glomuvenosa\/#%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-malformacion-glomuvenosa\" >Quais s\u00e3o as caracter\u00edsticas cl\u00ednicas da malforma\u00e7\u00e3o glomuvenosa?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/malformacion-glomuvenosa\/#%C2%BFComo-se-diagnostica-la-malformacion-glomuvenosa\" >Como \u00e9 diagnosticada uma malforma\u00e7\u00e3o glomensal?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/doctorhoogstra.com\/pt\/wiki\/malformacion-glomuvenosa\/#%C2%BFComo-se-trata-la-malformacion-glomuvenosa\" >Como \u00e9 tratada a malforma\u00e7\u00e3o glomensal?<\/a><\/li><\/ul><\/nav><\/div>\n\n<section class=\"textBlock\">\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQue-es-un-glomuvenoso-malformacion\"><\/span>O que \u00e9 um glomuvenous? <span class=\"term\" data-term-id=\"1631\">malforma\u00e7\u00e3o<\/span>? <span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>A malforma\u00e7\u00e3o glomurosa \u00e9 uma forma incomum de <span class=\"term\" data-term-id=\"1178\">venoso<\/span> malforma\u00e7\u00e3o, geralmente diagnosticada no nascimento ou mais tarde na inf\u00e2ncia ou na inf\u00e2ncia. A malforma\u00e7\u00e3o glomuveu tamb\u00e9m \u00e9 conhecida como glomangioma ou <span>glomangiomatose<\/span>.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFQuien-contrae-malformacion-glomuvenosa\"><\/span>Quem recebe uma malforma\u00e7\u00e3o glomuvenescedora?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Embora a malforma\u00e7\u00e3o glomensal possa ser espor\u00e1dica, tamb\u00e9m pode ser <span class=\"term\" data-term-id=\"849\">fam\u00edlia<\/span> com um <span class=\"term\" data-term-id=\"828\">autoss\u00f4mico<\/span> Padr\u00e3o dominante de heran\u00e7a (\u00e9 aqui que metade dos filhos de um pai afetado herda a condi\u00e7\u00e3o). Um anormal <span class=\"term\" data-term-id=\"1271\">cromossoma<\/span> 1p21-p22 foi identificado nessas fam\u00edlias, resultando na inativa\u00e7\u00e3o de uma prote\u00edna chamada glomulina.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n<div id=\"dermnet-dermnet-mobbox\">\n<\/div><\/div><\/div><\/div>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFCuales-son-las-caracteristicas-clinicas-de-la-malformacion-glomuvenosa\"><\/span>Quais s\u00e3o as caracter\u00edsticas cl\u00ednicas da malforma\u00e7\u00e3o glomuvenosa?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Uma malforma\u00e7\u00e3o glomensal apresenta-se como <span class=\"term\" data-term-id=\"324\">localizado<\/span> ou <span class=\"term\" data-term-id=\"619\">segmento<\/span> cole\u00e7\u00e3o de suaves, rosa, vermelho ou azul <span class=\"term\" data-term-id=\"367\">n\u00f3dulos<\/span> ou <span class=\"term\" data-term-id=\"38\">unindo<\/span> <span class=\"term\" data-term-id=\"368\">pratos<\/span>. Eles podem surgir em qualquer lugar da pele e raramente podem afetar <span class=\"term\" data-term-id=\"188\">mucosa<\/span> membranas voc\u00ea \u00e9 <span class=\"term\" data-term-id=\"753\">vascular<\/span> As les\u00f5es s\u00e3o menos compress\u00edveis do que outras formas de malforma\u00e7\u00e3o venosa. <\/p>\n<p>Les\u00f5es tendem a aumentar. <span class=\"term\" data-term-id=\"309\">estendido<\/span>mais espessa e mais profunda com a idade. Embora os n\u00f3dulos iniciem sem dor, eles podem se tornar sens\u00edveis ao toque.  <\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-diagnostica-la-malformacion-glomuvenosa\"><\/span>Como \u00e9 diagnosticada uma malforma\u00e7\u00e3o glomensal?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Pode-se suspeitar de malforma\u00e7\u00e3o glomuveu devido \u00e0 sua apar\u00eancia cl\u00ednica; por\u00e9m, <span class=\"term\" data-term-id=\"24\">bi\u00f3psia<\/span> Isso tamb\u00e9m pode ser feito. a <span class=\"term\" data-term-id=\"128\">histologia<\/span> A malforma\u00e7\u00e3o glomurosa \/ glomangioma se assemelha \u00e0 malforma\u00e7\u00e3o venosa com veias grandes, dilatadas e paredes finas no <span class=\"term\" data-term-id=\"61\">derme<\/span> e <span class=\"term\" data-term-id=\"900\">subcut\u00e2neo<\/span> tecido. Aglomerados de c\u00e9lulas gl\u00f4micas positivas para alfa-actina (<span class=\"term\" data-term-id=\"22\">benigno<\/span> <span class=\"term\" data-term-id=\"289\">tumor<\/span> c\u00e9lulas no <span class=\"term\" data-term-id=\"1183\">Tecido macio<\/span>) alinham os espa\u00e7os venosos. <span><br \/><\/span><\/p>\n<h2><span class=\"ez-toc-section\" id=\"%C2%BFComo-se-trata-la-malformacion-glomuvenosa\"><\/span>Como \u00e9 tratada a malforma\u00e7\u00e3o glomensal?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Cir\u00fargico <span class=\"term\" data-term-id=\"848\">excis\u00e3o<\/span> A malforma\u00e7\u00e3o glomurosa \u00e9 dif\u00edcil. As op\u00e7\u00f5es de tratamento incluem <span class=\"term\" data-term-id=\"1617\">Ser estar<\/span> e escleroterapia.<\/p>\n<\/section>","protected":false},"excerpt":{"rendered":"<p>\u00bfQu\u00e9 es un glomuvenoso? malformaci\u00f3n? La malformaci\u00f3n glomuvenosa es una forma inusual de venoso malformaci\u00f3n, t\u00edpicamente diagnosticada al nacer o m\u00e1s tarde en la infancia o la ni\u00f1ez. La malformaci\u00f3n&#8230;<\/p>","protected":false},"author":8,"featured_media":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","format":"standard","meta":{"footnotes":""},"categories":[],"tags":[],"class_list":["post-8244","wiki","type-wiki","status-publish","format-standard"],"_links":{"self":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki\/8244","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki"}],"about":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/types\/wiki"}],"author":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/users\/8"}],"replies":[{"embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/comments?post=8244"}],"version-history":[{"count":0,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/wiki\/8244\/revisions"}],"wp:attachment":[{"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/media?parent=8244"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/categories?post=8244"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/doctorhoogstra.com\/pt\/wp-json\/wp\/v2\/tags?post=8244"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}