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Acquired blascocoid dermatitis

What is acquired blaschkoid dermatitis?

Acquired blaschkoid dermatitis is a rare skin condition of unknown cause. It was first described in 1990 by Grosshans and Marot in Bordex, France.

It is also known as Blaschkitis, or idiopathic dermatitis along Blaschko's lines. It may represent the adult form of lichen striatum.

Acquired blascocoid dermatitis

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Lichen planus in the Blaschko distribution

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Linear psoriasis following Blaschko's lines

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Acquired blaschkitis

What are the clinical features of acquired blascoid dermatitis?

This condition is a inflammatory dermatitis-like skin condition or eczema and presents with dry, red, and irritable skin lesions. It is not present at birth, hence the term 'acquired'.

Acquired blascoid dermatitis is unilateral - only affects one side of the body. As the name suggests, skin lesions occur throughout Blaschko lines.

Lesions may resolve spontaneously but tend to relapse over time, especially in times of stress.

How was the diagnosis made?

The diagnosis of acquired blascoid dermatitis is made clinically due to its characteristic appearance.

Sometimes a skin biopsy it is required to distinguish it from other skin conditions that can arise in Blaschko's lines. Histopathological exam sample spongy dermatitis.

What is the treatment for acquired blaschkoid dermatitis?

Mild blascoid dermatitis may not require any specific treatment. Dryness can be managed with a emollient.

Usually current Steroid creams are not effective. There are several case reports where systemic steroid therapy was effective.